KEGG   PATHWAY: pcad00250
Entry
pcad00250                   Pathway                                
Name
Alanine, aspartate and glutamate metabolism - Physeter macrocephalus (sperm whale)
Class
Metabolism; Amino acid metabolism
Pathway map
pcad00250  Alanine, aspartate and glutamate metabolism
pcad00250

Module
pcad_M00027  GABA (gamma-Aminobutyrate) shunt [PATH:pcad00250]
Other DBs
GO: 0006522 0006531 0006536
Organism
Physeter macrocephalus (sperm whale) [GN:pcad]
Gene
102973240  CPS1; carbamoyl-phosphate synthase [ammonia], mitochondrial [KO:K01948] [EC:6.3.4.16]
102974310  NIT2; omega-amidase NIT2 isoform X1 [KO:K13566] [EC:3.5.1.3]
102974755  AGXT2; alanine--glyoxylate aminotransferase 2, mitochondrial [KO:K00827] [EC:2.6.1.44 2.6.1.40]
102974994  ALDH5A1; succinate-semialdehyde dehydrogenase, mitochondrial isoform X1 [KO:K00139] [EC:1.2.1.24]
102975069  [KO:K18310] [EC:6.3.1.17 6.3.2.41]
102975475  ASRGL1; isoaspartyl peptidase/L-asparaginase [KO:K13051] [EC:3.5.1.1 3.4.19.5]
102976825  IL4I1; L-amino-acid oxidase isoform X2 [KO:K03334] [EC:1.4.3.2]
102977573  GPT2; alanine aminotransferase 2 isoform X1 [KO:K00814] [EC:2.6.1.2]
102978503  GLS; glutaminase kidney isoform, mitochondrial isoform X4 [KO:K01425] [EC:3.5.1.2]
102978941  [KO:K00261] [EC:1.4.1.3]
102979403  AGXT; alanine--glyoxylate aminotransferase [KO:K00830] [EC:2.6.1.44 2.6.1.45 2.6.1.51]
102979651  FOLH1; glutamate carboxypeptidase 2 isoform X1 [KO:K14592] [EC:3.4.17.21]
102979919  ADSS1; adenylosuccinate synthetase isozyme 1 isoform X1 [KO:K01939] [EC:6.3.4.4]
102980581  NAT8L; N-acetylaspartate synthetase [KO:K18309] [EC:2.3.1.17]
102980772  ADSL; adenylosuccinate lyase isoform X3 [KO:K01756] [EC:4.3.2.2]
102981532  RIMKLB; beta-citrylglutamate synthase B isoform X1 [KO:K18310] [EC:6.3.1.17 6.3.2.41]
102982103  RIMKLA; N-acetylaspartylglutamate synthase A [KO:K18311] [EC:6.3.2.41 6.3.2.42]
102982667  ALDH4A1; delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial isoform X2 [KO:K00294] [EC:1.2.1.88]
102982760  ASPA; aspartoacylase [KO:K01437] [EC:3.5.1.15]
102983048  ASL; argininosuccinate lyase [KO:K01755] [EC:4.3.2.1]
102983900  ASNS; asparagine synthetase [glutamine-hydrolyzing] isoform X1 [KO:K01953] [EC:6.3.5.4]
102984421  ADSS2; adenylosuccinate synthetase isozyme 2 [KO:K01939] [EC:6.3.4.4]
102984473  [KO:K00261] [EC:1.4.1.3]
102984477  GLS2; glutaminase liver isoform, mitochondrial isoform X1 [KO:K01425] [EC:3.5.1.2]
102987420  GFPT1; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 1 isoform X4 [KO:K00820] [EC:2.6.1.16]
102988036  ASS1; argininosuccinate synthase [KO:K01940] [EC:6.3.4.5]
102988062  CAD; CAD protein isoform X3 [KO:K11540] [EC:6.3.5.5 2.1.3.2 3.5.2.3]
102988357  GAD2; glutamate decarboxylase 2 [KO:K01580] [EC:4.1.1.15]
102988708  GLUD1; glutamate dehydrogenase 1, mitochondrial [KO:K00261] [EC:1.4.1.3]
102988769  [KO:K03334] [EC:1.4.3.2]
102989047  GLUL; glutamine synthetase isoform X1 [KO:K01915] [EC:6.3.1.2]
102989668  GOT1; aspartate aminotransferase, cytoplasmic isoform X1 [KO:K14454] [EC:2.6.1.1]
102990755  DDO; D-aspartate oxidase isoform X2 [KO:K00272] [EC:1.4.3.1]
102991113  GOT2; aspartate aminotransferase, mitochondrial isoform X3 [KO:K14455] [EC:2.6.1.1]
102994081  PPAT; amidophosphoribosyltransferase isoform X2 [KO:K00764] [EC:2.4.2.14]
102995298  ABAT; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
102995985  GAD1; glutamate decarboxylase 1 isoform X1 [KO:K01580] [EC:4.1.1.15]
102996056  GFPT2; glutamine--fructose-6-phosphate aminotransferase [isomerizing] 2 isoform X2 [KO:K00820] [EC:2.6.1.16]
112062611  GPT; alanine aminotransferase 1 isoform X1 [KO:K00814] [EC:2.6.1.2]
Compound
C00014  Ammonia
C00022  Pyruvate
C00025  L-Glutamate
C00026  2-Oxoglutarate
C00036  Oxaloacetate
C00041  L-Alanine
C00042  Succinate
C00049  L-Aspartate
C00064  L-Glutamine
C00122  Fumarate
C00152  L-Asparagine
C00158  Citrate
C00169  Carbamoyl phosphate
C00232  Succinate semialdehyde
C00334  4-Aminobutanoate
C00352  D-Glucosamine 6-phosphate
C00402  D-Aspartate
C00438  N-Carbamoyl-L-aspartate
C00940  2-Oxoglutaramate
C01042  N-Acetyl-L-aspartate
C02362  2-Oxosuccinamate
C03090  5-Phosphoribosylamine
C03406  N-(L-Arginino)succinate
C03794  N6-(1,2-Dicarboxyethyl)-AMP
C03912  (S)-1-Pyrroline-5-carboxylate
C12270  N-Acetylaspartylglutamate
C20775  beta-Citryl-L-glutamate
C20776  N-Acetylaspartylglutamylglutamate
Reference
  Authors
Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds).
  Title
[Cellular Functions and Metabolic Maps] (In Japanese)
  Journal
Tokyo Kagaku Dojin (1997)
Reference
PMID:9687539
  Authors
Wu G
  Title
Intestinal mucosal amino acid catabolism.
  Journal
J Nutr 128:1249-52 (1998)
DOI:10.1093/jn/128.8.1249
Related
pathway
pcad00010  Glycolysis / Gluconeogenesis
pcad00020  Citrate cycle (TCA cycle)
pcad00220  Arginine biosynthesis
pcad00230  Purine metabolism
pcad00240  Pyrimidine metabolism
pcad00260  Glycine, serine and threonine metabolism
pcad00330  Arginine and proline metabolism
pcad00340  Histidine metabolism
pcad00410  beta-Alanine metabolism
pcad00470  D-Amino acid metabolism
pcad00480  Glutathione metabolism
pcad00520  Amino sugar and nucleotide sugar metabolism
pcad00620  Pyruvate metabolism
pcad00630  Glyoxylate and dicarboxylate metabolism
pcad00650  Butanoate metabolism
pcad00760  Nicotinate and nicotinamide metabolism
pcad00770  Pantothenate and CoA biosynthesis
pcad00860  Porphyrin metabolism
pcad00910  Nitrogen metabolism
KO pathway
ko00250   

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