KEGG   PATHWAY: spu00280
Entry
spu00280                    Pathway                                
Name
Valine, leucine and isoleucine degradation - Strongylocentrotus purpuratus (purple sea urchin)
Class
Metabolism; Amino acid metabolism
Pathway map
spu00280  Valine, leucine and isoleucine degradation
spu00280

Module
spu_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA [PATH:spu00280]
spu_M00741  Propanoyl-CoA metabolism, propanoyl-CoA => succinyl-CoA [PATH:spu00280]
Other DBs
GO: 0006550 0006552 0006574
Organism
Strongylocentrotus purpuratus (purple sea urchin) [GN:spu]
Gene
583254  branched-chain-amino-acid aminotransferase, cytosolic [KO:K00826] [EC:2.6.1.42]
115919491  branched-chain-amino-acid aminotransferase, cytosolic-like [KO:K00826] [EC:2.6.1.42]
583728  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial [KO:K00166] [EC:1.2.4.4]
592151  2-oxoisovalerate dehydrogenase subunit beta, mitochondrial [KO:K00167] [EC:1.2.4.4]
115928268  LOW QUALITY PROTEIN: 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial-like [KO:K00167] [EC:1.2.4.4]
582235  lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial isoform X1 [KO:K09699] [EC:2.3.1.168]
577103  dihydrolipoyl dehydrogenase, mitochondrial [KO:K00382] [EC:1.8.1.4]
579817  short-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00248] [EC:1.3.8.1]
591118  probable medium-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00249] [EC:1.3.8.7]
105444714  probable medium-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00249] [EC:1.3.8.7]
591888  isovaleryl-CoA dehydrogenase, mitochondrial isoform X1 [KO:K00253] [EC:1.3.8.4]
589757  isovaleryl-CoA dehydrogenase, mitochondrial [KO:K00253] [EC:1.3.8.4]
589735  isovaleryl-CoA dehydrogenase, mitochondrial [KO:K00253] [EC:1.3.8.4]
593139  short/branched chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K09478] [EC:1.3.8.5]
585357  trifunctional enzyme subunit alpha, mitochondrial [KO:K07515] [EC:4.2.1.17 1.1.1.211]
588204  peroxisomal bifunctional enzyme isoform X1 [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
753669  peroxisomal bifunctional enzyme-like isoform X1 [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
575690  Echs1; enoyl CoA hydratase, short chain, 1, mitochondrial [KO:K07511] [EC:4.2.1.17]
582126  hydroxyacyl-coenzyme A dehydrogenase, mitochondrial [KO:K00022] [EC:1.1.1.35]
579135  3-hydroxyacyl-CoA dehydrogenase type-2 [KO:K08683] [EC:1.1.1.35 1.1.1.178]
587557  3-ketoacyl-CoA thiolase A, peroxisomal [KO:K07513] [EC:2.3.1.16]
115918115  3-ketoacyl-CoA thiolase A, peroxisomal-like [KO:K07513] [EC:2.3.1.16]
588288  3-ketoacyl-CoA thiolase, mitochondrial [KO:K07508] [EC:2.3.1.16]
115927202  3-ketoacyl-CoA thiolase, mitochondrial-like [KO:K07508] [EC:2.3.1.16]
585332  uncharacterized protein B0303.3 isoform X1 [KO:K07509] [EC:2.3.1.16]
582365  propionyl-CoA carboxylase alpha chain, mitochondrial isoform X1 [KO:K01965] [EC:6.4.1.3]
592281  propionyl-CoA carboxylase beta chain, mitochondrial [KO:K01966] [EC:6.4.1.3 2.1.3.15]
576505  methylmalonyl-CoA epimerase, mitochondrial [KO:K05606] [EC:5.1.99.1]
576452  methylmalonyl-CoA mutase, mitochondrial isoform X1 [KO:K01847] [EC:5.4.99.2]
586315  3-hydroxyisobutyryl-CoA hydrolase, mitochondrial [KO:K05605] [EC:3.1.2.4]
587548  3-hydroxyisobutyrate dehydrogenase, mitochondrial [KO:K00020] [EC:1.1.1.31]
578337  methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial [KO:K00140] [EC:1.2.1.18 1.2.1.27]
581754  aldehyde dehydrogenase, mitochondrial [KO:K00128] [EC:1.2.1.3]
581706  aldehyde dehydrogenase, mitochondrial [KO:K00128] [EC:1.2.1.3]
105445554  aldehyde dehydrogenase, dimeric NADP-preferring [KO:K00128] [EC:1.2.1.3]
593236  aldehyde dehydrogenase family 16 member A1 [KO:K00128] [EC:1.2.1.3]
105445170  aldehyde dehydrogenase family 3 member A2 isoform X1 [KO:K00128] [EC:1.2.1.3]
756945  aldehyde dehydrogenase, dimeric NADP-preferring [KO:K00128] [EC:1.2.1.3]
588376  alpha-aminoadipic semialdehyde dehydrogenase [KO:K14085] [EC:1.2.1.31 1.2.1.8 1.2.1.3]
580956  4-trimethylaminobutyraldehyde dehydrogenase [KO:K00149] [EC:1.2.1.47 1.2.1.3]
583864  4-trimethylaminobutyraldehyde dehydrogenase A [KO:K00149] [EC:1.2.1.47 1.2.1.3]
115918585  4-trimethylaminobutyraldehyde dehydrogenase-like [KO:K00149] [EC:1.2.1.47 1.2.1.3]
579933  malonate--CoA ligase ACSF3, mitochondrial [KO:K18660] [EC:6.2.1.76 6.2.1.-]
577656  4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
594821  alanine--glyoxylate aminotransferase 2, mitochondrial [KO:K00827] [EC:2.6.1.44 2.6.1.40]
753561  methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial-like [KO:K01968] [EC:6.4.1.4]
579180  methylcrotonoyl-CoA carboxylase beta chain, mitochondrial [KO:K01969] [EC:6.4.1.4]
584783  methylcrotonoyl-CoA carboxylase beta chain, mitochondrial [KO:K01969] [EC:6.4.1.4]
115919288  methylcrotonoyl-CoA carboxylase beta chain, mitochondrial-like [KO:K01969] [EC:6.4.1.4]
100889966  methylcrotonoyl-CoA carboxylase beta chain, mitochondrial [KO:K01969] [EC:6.4.1.4]
577505  methylglutaconyl-CoA hydratase, mitochondrial isoform X1 [KO:K05607] [EC:4.2.1.18]
756856  hydroxymethylglutaryl-CoA lyase, mitochondrial [KO:K01640] [EC:4.1.3.4]
589818  succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial [KO:K01027] [EC:2.8.3.5]
115918988  succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial-like [KO:K01027] [EC:2.8.3.5]
590598  acetoacetyl-CoA synthetase [KO:K01907] [EC:6.2.1.16]
763037  acetyl-CoA acetyltransferase, cytosolic [KO:K00626] [EC:2.3.1.9]
584928  acetyl-CoA acetyltransferase, mitochondrial [KO:K00626] [EC:2.3.1.9]
115927929  acetyl-CoA acetyltransferase, cytosolic-like [KO:K00626] [EC:2.3.1.9]
579089  acetyl-CoA acetyltransferase, cytosolic-like [KO:K00626] [EC:2.3.1.9]
115928354  acetyl-CoA acetyltransferase, cytosolic-like [KO:K00626] [EC:2.3.1.9]
578259  hydroxymethylglutaryl-CoA synthase 1 isoform X1 [KO:K01641] [EC:2.3.3.10]
Compound
C00024  Acetyl-CoA
C00068  Thiamin diphosphate
C00091  Succinyl-CoA
C00100  Propanoyl-CoA
C00123  L-Leucine
C00141  3-Methyl-2-oxobutanoic acid
C00164  Acetoacetate
C00183  L-Valine
C00233  4-Methyl-2-oxopentanoate
C00332  Acetoacetyl-CoA
C00349  2-Methyl-3-oxopropanoate
C00356  (S)-3-Hydroxy-3-methylglutaryl-CoA
C00407  L-Isoleucine
C00630  2-Methylpropanoyl-CoA
C00671  (S)-3-Methyl-2-oxopentanoic acid
C00683  (S)-Methylmalonyl-CoA
C01205  (R)-3-Amino-2-methylpropanoate
C01213  (R)-Methylmalonyl-CoA
C02170  Methylmalonate
C02939  3-Methylbutanoyl-CoA
C03069  3-Methylcrotonyl-CoA
C03231  3-Methylglutaconyl-CoA
C03284  L-3-Aminoisobutanoate
C03344  2-Methylacetoacetyl-CoA
C03345  2-Methylbut-2-enoyl-CoA
C03460  2-Methylprop-2-enoyl-CoA
C04405  (2S,3S)-3-Hydroxy-2-methylbutanoyl-CoA
C05996  Branched chain fatty acid
C05998  3-Hydroxyisovaleryl-CoA
C06000  (S)-3-Hydroxyisobutyryl-CoA
C06001  (S)-3-Hydroxyisobutyrate
C06002  (S)-Methylmalonate semialdehyde
C15972  Enzyme N6-(lipoyl)lysine
C15973  Enzyme N6-(dihydrolipoyl)lysine
C15974  3-Methyl-1-hydroxybutyl-ThPP
C15975  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(3-methylbutanoyl)dihydrolipoyllysine
C15976  2-Methyl-1-hydroxypropyl-ThPP
C15977  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine
C15978  2-Methyl-1-hydroxybutyl-ThPP
C15979  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylbutanoyl)dihydrolipoyllysine
C15980  (S)-2-Methylbutanoyl-CoA
C20827  3-Hydroxyisovalerate
Related
pathway
spu00020  Citrate cycle (TCA cycle)
spu00240  Pyrimidine metabolism
spu00290  Valine, leucine and isoleucine biosynthesis
spu00640  Propanoate metabolism
spu00900  Terpenoid backbone biosynthesis
KO pathway
ko00280   
LinkDB

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