KEGG   PATHWAY: cpoc00280
Entry
cpoc00280                   Pathway                                
Name
Valine, leucine and isoleucine degradation - Cavia porcellus (domestic guinea pig)
Class
Metabolism; Amino acid metabolism
Pathway map
cpoc00280  Valine, leucine and isoleucine degradation
cpoc00280

Module
cpoc_M00741  Propanoyl-CoA metabolism, propanoyl-CoA => succinyl-CoA [PATH:cpoc00280]
Other DBs
GO: 0006550 0006552 0006574
Organism
Cavia porcellus (domestic guinea pig) [GN:cpoc]
Gene
100135519  [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
100712874  Mccc2; methylcrotonoyl-CoA carboxylase beta chain, mitochondrial [KO:K01969] [EC:6.4.1.4]
100713291  Hmgcl; hydroxymethylglutaryl-CoA lyase, mitochondrial isoform X1 [KO:K01640] [EC:4.1.3.4]
100714172  Aox4; aldehyde oxidase 4 [KO:K00157] [EC:1.2.3.1]
100714301  Agxt2; alanine--glyoxylate aminotransferase 2, mitochondrial isoform X1 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
100714379  Acat2; acetyl-CoA acetyltransferase, cytosolic [KO:K00626] [EC:2.3.1.9]
100714817  Acadsb; short/branched chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K09478] [EC:1.3.8.5]
100714971  Ivd; isovaleryl-CoA dehydrogenase, mitochondrial [KO:K00253] [EC:1.3.8.4]
100715185  Bckdha; 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial [KO:K00166] [EC:1.2.4.4]
100715434  Acaa2; 3-ketoacyl-CoA thiolase, mitochondrial [KO:K07508] [EC:2.3.1.16]
100715623  Mcee; methylmalonyl-CoA epimerase, mitochondrial isoform X1 [KO:K05606] [EC:5.1.99.1]
100715786  Hadh; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial [KO:K00022] [EC:1.1.1.35]
100715842  Acadm; medium-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00249] [EC:1.3.8.7]
100717423  Acat1; acetyl-CoA acetyltransferase, mitochondrial isoform X1 [KO:K00626] [EC:2.3.1.9]
100717591  Mccc1; methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial isoform X1 [KO:K01968] [EC:6.4.1.4]
100718257  Aacs; acetoacetyl-CoA synthetase [KO:K01907] [EC:6.2.1.16]
100718728  Oxct2; succinyl-CoA:3-ketoacid coenzyme A transferase 2, mitochondrial [KO:K01027] [EC:2.8.3.5]
100718814  Hsd17b10; 3-hydroxyacyl-CoA dehydrogenase type-2 [KO:K08683] [EC:1.1.1.35 1.1.1.178]
100719938  Aox2; aldehyde oxidase 2 [KO:K00157] [EC:1.2.3.1]
100720210  Aox1; aldehyde oxidase 1 [KO:K00157] [EC:1.2.3.1]
100721798  Dld; dihydrolipoyl dehydrogenase, mitochondrial [KO:K00382] [EC:1.8.1.4]
100722053  Il4i1; L-amino-acid oxidase isoform X1 [KO:K03334] [EC:1.4.3.2]
100722166  Bcat1; branched-chain-amino-acid aminotransferase, cytosolic isoform X3 [KO:K00826] [EC:2.6.1.42]
100722514  Acaa1; 3-ketoacyl-CoA thiolase, peroxisomal [KO:K07513] [EC:2.3.1.16]
100722933  Pcca; propionyl-CoA carboxylase alpha chain, mitochondrial isoform X3 [KO:K01965] [EC:6.4.1.3]
100723555  Hadha; trifunctional enzyme subunit alpha, mitochondrial [KO:K07515] [EC:4.2.1.17 1.1.1.211]
100725220  Hadhb; trifunctional enzyme subunit beta, mitochondrial [KO:K07509] [EC:2.3.1.16]
100725419  Abat; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
100725796  Hibch; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial isoform X1 [KO:K05605] [EC:3.1.2.4]
100727078  Hmgcs2; hydroxymethylglutaryl-CoA synthase, mitochondrial [KO:K01641] [EC:2.3.3.10]
100727478  Aldh16a1; aldehyde dehydrogenase family 16 member A1 isoform X1 [KO:K00128] [EC:1.2.1.3]
100728115  Bcat2; branched-chain-amino-acid aminotransferase, mitochondrial isoform X2 [KO:K00826] [EC:2.6.1.42]
100728163  Mut; methylmalonyl-CoA mutase, mitochondrial [KO:K01847] [EC:5.4.99.2]
100728489  Echs1; enoyl-CoA hydratase, mitochondrial [KO:K07511] [EC:4.2.1.17]
100728950  Aldh3a2; fatty aldehyde dehydrogenase isoform X1 [KO:K00128] [EC:1.2.1.3]
100729570  Pccb; propionyl-CoA carboxylase beta chain, mitochondrial isoform X2 [KO:K01966] [EC:6.4.1.3 2.1.3.15]
100729577  Acsf3; acyl-CoA synthetase family member 3, mitochondrial isoform X1 [KO:K18660] [EC:6.2.1.76 6.2.1.-]
100730314  Aldh2; aldehyde dehydrogenase, mitochondrial [KO:K00128] [EC:1.2.1.3]
100731247  Dbt; lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial [KO:K09699] [EC:2.3.1.168]
100731467  Hmgcs1; hydroxymethylglutaryl-CoA synthase, cytoplasmic [KO:K01641] [EC:2.3.3.10]
100731951  Bckdhb; 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X1 [KO:K00167] [EC:1.2.4.4]
100732213  Aldh6a1; methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial [KO:K00140] [EC:1.2.1.18 1.2.1.27]
100732238  Aldh7a1; alpha-aminoadipic semialdehyde dehydrogenase [KO:K14085] [EC:1.2.1.31 1.2.1.8 1.2.1.3]
100732288  Aldh9a1; 4-trimethylaminobutyraldehyde dehydrogenase [KO:K00149] [EC:1.2.1.47 1.2.1.3]
100732696  [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
100732790  Hmgcll1; 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic isoform X6 [KO:K01640] [EC:4.1.3.4]
100733415  Oxct1; succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial [KO:K01027] [EC:2.8.3.5]
100733918  Acads; short-chain specific acyl-CoA dehydrogenase, mitochondrial isoform X2 [KO:K00248] [EC:1.3.8.1]
100734441  Aldh1b1; LOW QUALITY PROTEIN: aldehyde dehydrogenase X, mitochondrial [KO:K00128] [EC:1.2.1.3]
100734642  Acad8; isobutyryl-CoA dehydrogenase, mitochondrial isoform X1 [KO:K11538] [EC:1.3.99.-]
100735244  [KO:K03334] [EC:1.4.3.2]
Compound
C00024  Acetyl-CoA
C00068  Thiamin diphosphate
C00091  Succinyl-CoA
C00100  Propanoyl-CoA
C00123  L-Leucine
C00141  3-Methyl-2-oxobutanoic acid
C00164  Acetoacetate
C00183  L-Valine
C00233  4-Methyl-2-oxopentanoate
C00332  Acetoacetyl-CoA
C00349  2-Methyl-3-oxopropanoate
C00356  (S)-3-Hydroxy-3-methylglutaryl-CoA
C00407  L-Isoleucine
C00630  2-Methylpropanoyl-CoA
C00671  (S)-3-Methyl-2-oxopentanoic acid
C00683  (S)-Methylmalonyl-CoA
C01205  (R)-3-Amino-2-methylpropanoate
C01213  (R)-Methylmalonyl-CoA
C02170  Methylmalonate
C02939  3-Methylbutanoyl-CoA
C03069  3-Methylcrotonyl-CoA
C03231  3-Methylglutaconyl-CoA
C03284  L-3-Aminoisobutanoate
C03344  2-Methylacetoacetyl-CoA
C03345  2-Methylbut-2-enoyl-CoA
C03460  2-Methylprop-2-enoyl-CoA
C04405  (2S,3S)-3-Hydroxy-2-methylbutanoyl-CoA
C05996  Branched chain fatty acid
C05998  3-Hydroxyisovaleryl-CoA
C06000  (S)-3-Hydroxyisobutyryl-CoA
C06001  (S)-3-Hydroxyisobutyrate
C06002  (S)-Methylmalonate semialdehyde
C15972  Enzyme N6-(lipoyl)lysine
C15973  Enzyme N6-(dihydrolipoyl)lysine
C15974  3-Methyl-1-hydroxybutyl-ThPP
C15975  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(3-methylbutanoyl)dihydrolipoyllysine
C15976  2-Methyl-1-hydroxypropyl-ThPP
C15977  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine
C15978  2-Methyl-1-hydroxybutyl-ThPP
C15979  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylbutanoyl)dihydrolipoyllysine
C15980  (S)-2-Methylbutanoyl-CoA
C20827  3-Hydroxyisovalerate
Related
pathway
cpoc00020  Citrate cycle (TCA cycle)
cpoc00240  Pyrimidine metabolism
cpoc00290  Valine, leucine and isoleucine biosynthesis
cpoc00640  Propanoate metabolism
cpoc00900  Terpenoid backbone biosynthesis
KO pathway
ko00280   

DBGET integrated database retrieval system