KEGG   PATHWAY: tmu00280
Entry
tmu00280                    Pathway                                
Name
Valine, leucine and isoleucine degradation - Trichechus manatus latirostris (Florida manatee)
Class
Metabolism; Amino acid metabolism
Pathway map
tmu00280  Valine, leucine and isoleucine degradation
tmu00280

Module
tmu_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA [PATH:tmu00280]
tmu_M00741  Propanoyl-CoA metabolism, propanoyl-CoA => succinyl-CoA [PATH:tmu00280]
Other DBs
GO: 0006550 0006552 0006574
Organism
Trichechus manatus latirostris (Florida manatee) [GN:tmu]
Gene
101357817  branched-chain-amino-acid aminotransferase, mitochondrial [KO:K00826] [EC:2.6.1.42]
101355121  branched-chain-amino-acid aminotransferase, cytosolic [KO:K00826] [EC:2.6.1.42]
101351869  L-amino-acid oxidase [KO:K03334] [EC:1.4.3.2]
101342469  L-amino-acid oxidase-like [KO:K03334] [EC:1.4.3.2]
101357695  L-amino-acid oxidase-like [KO:K03334] [EC:1.4.3.2]
101343046  2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial [KO:K00166] [EC:1.2.4.4]
101359226  2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X1 [KO:K00167] [EC:1.2.4.4]
101344068  lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial [KO:K09699] [EC:2.3.1.168]
101351699  dihydrolipoyl dehydrogenase, mitochondrial isoform X1 [KO:K00382] [EC:1.8.1.4]
101356048  short-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00248] [EC:1.3.8.1]
101357421  medium-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00249] [EC:1.3.8.7]
101347930  isovaleryl-CoA dehydrogenase, mitochondrial isoform X1 [KO:K00253] [EC:1.3.8.4]
101353141  short/branched chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K09478] [EC:1.3.8.5]
101352722  isobutyryl-CoA dehydrogenase, mitochondrial [KO:K11538] [EC:1.3.99.-]
101353485  trifunctional enzyme subunit alpha, mitochondrial [KO:K07515] [EC:4.2.1.17 1.1.1.211]
101352903  peroxisomal bifunctional enzyme [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
101361856  enoyl-CoA hydratase, mitochondrial [KO:K07511] [EC:4.2.1.17]
101344876  hydroxyacyl-coenzyme A dehydrogenase, mitochondrial [KO:K00022] [EC:1.1.1.35]
101360197  3-hydroxyacyl-CoA dehydrogenase type-2 [KO:K08683] [EC:1.1.1.35 1.1.1.178]
101341576  3-ketoacyl-CoA thiolase, peroxisomal isoform X1 [KO:K07513] [EC:2.3.1.16]
101353742  trifunctional enzyme subunit beta, mitochondrial [KO:K07509] [EC:2.3.1.16]
101357580  propionyl-CoA carboxylase alpha chain, mitochondrial isoform X1 [KO:K01965] [EC:6.4.1.3]
101354598  propionyl-CoA carboxylase beta chain, mitochondrial isoform X1 [KO:K01966] [EC:6.4.1.3 2.1.3.15]
101340531  methylmalonyl-CoA epimerase, mitochondrial [KO:K05606] [EC:5.1.99.1]
101343064  methylmalonyl-CoA mutase, mitochondrial isoform X1 [KO:K01847] [EC:5.4.99.2]
101358694  3-hydroxyisobutyryl-CoA hydrolase, mitochondrial isoform X1 [KO:K05605] [EC:3.1.2.4]
101344868  3-hydroxyisobutyrate dehydrogenase, mitochondrial [KO:K00020] [EC:1.1.1.31]
101351397  methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial isoform X2 [KO:K00140] [EC:1.2.1.18 1.2.1.27]
101351079  aldehyde dehydrogenase family 16 member A1 isoform X1 [KO:K00128] [EC:1.2.1.3]
101345643  fatty aldehyde dehydrogenase isoform X1 [KO:K00128] [EC:1.2.1.3]
101355077  LOW QUALITY PROTEIN: aldehyde dehydrogenase X, mitochondrial [KO:K00128] [EC:1.2.1.3]
101349890  aldehyde dehydrogenase, mitochondrial [KO:K00128] [EC:1.2.1.3]
101361542  alpha-aminoadipic semialdehyde dehydrogenase [KO:K14085] [EC:1.2.1.31 1.2.1.8 1.2.1.3]
101357831  4-trimethylaminobutyraldehyde dehydrogenase [KO:K00149] [EC:1.2.1.47 1.2.1.3]
101340907  aldehyde oxidase [KO:K00157] [EC:1.2.3.1]
101341581  LOW QUALITY PROTEIN: aldehyde oxidase 2-like [KO:K00157] [EC:1.2.3.1]
101348352  acyl-CoA synthetase family member 3, mitochondrial [KO:K18660] [EC:6.2.1.76 6.2.1.-]
101359178  4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
101347029  alanine--glyoxylate aminotransferase 2, mitochondrial isoform X1 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
101343112  methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial isoform X2 [KO:K01968] [EC:6.4.1.4]
101343166  methylcrotonoyl-CoA carboxylase beta chain, mitochondrial [KO:K01969] [EC:6.4.1.4]
101350244  methylglutaconyl-CoA hydratase, mitochondrial isoform X1 [KO:K05607] [EC:4.2.1.18]
101351966  3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic isoform X1 [KO:K01640] [EC:4.1.3.4]
101355356  hydroxymethylglutaryl-CoA lyase, mitochondrial isoform X2 [KO:K01640] [EC:4.1.3.4]
105756036  succinyl-CoA:3-ketoacid coenzyme A transferase 2, mitochondrial-like [KO:K01027] [EC:2.8.3.5]
105756037  succinyl-CoA:3-ketoacid coenzyme A transferase 2, mitochondrial-like [KO:K01027] [EC:2.8.3.5]
101353012  succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial isoform X2 [KO:K01027] [EC:2.8.3.5]
101344064  acetoacetyl-CoA synthetase isoform X1 [KO:K01907] [EC:6.2.1.16]
101344749  acetyl-CoA acetyltransferase, cytosolic [KO:K00626] [EC:2.3.1.9]
101362050  acetyl-CoA acetyltransferase, mitochondrial isoform X1 [KO:K00626] [EC:2.3.1.9]
101354886  hydroxymethylglutaryl-CoA synthase, cytoplasmic isoform X1 [KO:K01641] [EC:2.3.3.10]
101359733  hydroxymethylglutaryl-CoA synthase, mitochondrial [KO:K01641] [EC:2.3.3.10]
Compound
C00024  Acetyl-CoA
C00068  Thiamin diphosphate
C00091  Succinyl-CoA
C00100  Propanoyl-CoA
C00123  L-Leucine
C00141  3-Methyl-2-oxobutanoic acid
C00164  Acetoacetate
C00183  L-Valine
C00233  4-Methyl-2-oxopentanoate
C00332  Acetoacetyl-CoA
C00349  2-Methyl-3-oxopropanoate
C00356  (S)-3-Hydroxy-3-methylglutaryl-CoA
C00407  L-Isoleucine
C00630  2-Methylpropanoyl-CoA
C00671  (S)-3-Methyl-2-oxopentanoic acid
C00683  (S)-Methylmalonyl-CoA
C01205  (R)-3-Amino-2-methylpropanoate
C01213  (R)-Methylmalonyl-CoA
C02170  Methylmalonate
C02939  3-Methylbutanoyl-CoA
C03069  3-Methylcrotonyl-CoA
C03231  3-Methylglutaconyl-CoA
C03284  L-3-Aminoisobutanoate
C03344  2-Methylacetoacetyl-CoA
C03345  2-Methylbut-2-enoyl-CoA
C03460  2-Methylprop-2-enoyl-CoA
C04405  (2S,3S)-3-Hydroxy-2-methylbutanoyl-CoA
C05996  Branched chain fatty acid
C05998  3-Hydroxyisovaleryl-CoA
C06000  (S)-3-Hydroxyisobutyryl-CoA
C06001  (S)-3-Hydroxyisobutyrate
C06002  (S)-Methylmalonate semialdehyde
C15972  Enzyme N6-(lipoyl)lysine
C15973  Enzyme N6-(dihydrolipoyl)lysine
C15974  3-Methyl-1-hydroxybutyl-ThPP
C15975  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(3-methylbutanoyl)dihydrolipoyllysine
C15976  2-Methyl-1-hydroxypropyl-ThPP
C15977  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine
C15978  2-Methyl-1-hydroxybutyl-ThPP
C15979  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylbutanoyl)dihydrolipoyllysine
C15980  (S)-2-Methylbutanoyl-CoA
C20827  3-Hydroxyisovalerate
Related
pathway
tmu00020  Citrate cycle (TCA cycle)
tmu00240  Pyrimidine metabolism
tmu00290  Valine, leucine and isoleucine biosynthesis
tmu00640  Propanoate metabolism
tmu00900  Terpenoid backbone biosynthesis
KO pathway
ko00280   
LinkDB

DBGET integrated database retrieval system