KEGG   PATHWAY: pbi00280
Entry
pbi00280                    Pathway                                
Name
Valine, leucine and isoleucine degradation - Python bivittatus (Burmese python)
Class
Metabolism; Amino acid metabolism
Pathway map
pbi00280  Valine, leucine and isoleucine degradation
pbi00280

Module
pbi_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA [PATH:pbi00280]
pbi_M00741  Propanoyl-CoA metabolism, propanoyl-CoA => succinyl-CoA [PATH:pbi00280]
Other DBs
GO: 0006550 0006552 0006574
Organism
Python bivittatus (Burmese python) [GN:pbi]
Gene
103047981  MCEE; methylmalonyl-CoA epimerase, mitochondrial [KO:K05606] [EC:5.1.99.1]
103048172  [KO:K01969] [EC:6.4.1.4]
103048324  ABAT; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
103048497  BCKDHA; 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1 [KO:K00166] [EC:1.2.4.4]
103048540  [KO:K01965] [EC:6.4.1.3]
103048615  AOX1; aldehyde oxidase [KO:K00157] [EC:1.2.3.1]
103049409  ACAA2; 3-ketoacyl-CoA thiolase, mitochondrial [KO:K07508] [EC:2.3.1.16]
103049565  ALDH7A1; alpha-aminoadipic semialdehyde dehydrogenase isoform X1 [KO:K14085] [EC:1.2.1.31 1.2.1.8 1.2.1.3]
103050760  DBT; lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial [KO:K09699] [EC:2.3.1.168]
103050915  [KO:K03334] [EC:1.4.3.2]
103051793  HSD17B10; 3-hydroxyacyl-CoA dehydrogenase type-2 [KO:K08683] [EC:1.1.1.35 1.1.1.178]
103051894  ALDH2; aldehyde dehydrogenase, mitochondrial [KO:K00128] [EC:1.2.1.3]
103052006  PCCB; propionyl-CoA carboxylase beta chain, mitochondrial [KO:K01966] [EC:6.4.1.3 2.1.3.15]
103052046  HMGCS2; hydroxymethylglutaryl-CoA synthase, mitochondrial [KO:K01641] [EC:2.3.3.10]
103052512  OXCT1; succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial [KO:K01027] [EC:2.8.3.5]
103052587  HADHB; trifunctional enzyme subunit beta, mitochondrial [KO:K07509] [EC:2.3.1.16]
103052873  EHHADH; peroxisomal bifunctional enzyme isoform X1 [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
103053277  HADHA; trifunctional enzyme subunit alpha, mitochondrial [KO:K07515] [EC:4.2.1.17 1.1.1.211]
103053826  [KO:K03334] [EC:1.4.3.2]
103053938  ALDH6A1; methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial [KO:K00140] [EC:1.2.1.18 1.2.1.27]
103054419  IVD; isovaleryl-CoA dehydrogenase, mitochondrial [KO:K00253] [EC:1.3.8.4]
103055918  ALDH16A1; aldehyde dehydrogenase family 16 member A1 isoform X3 [KO:K00128] [EC:1.2.1.3]
103056099  ACAT2; acetyl-CoA acetyltransferase, cytosolic [KO:K00626] [EC:2.3.1.9]
103056268  [KO:K07513] [EC:2.3.1.16]
103056557  [KO:K01640] [EC:4.1.3.4]
103056986  ALDH9A1; 4-trimethylaminobutyraldehyde dehydrogenase isoform X1 [KO:K00149] [EC:1.2.1.47 1.2.1.3]
103057279  HMGCS1; hydroxymethylglutaryl-CoA synthase, cytoplasmic isoform X1 [KO:K01641] [EC:2.3.3.10]
103058003  ACSF3; acyl-CoA synthetase family member 3, mitochondrial [KO:K18660] [EC:6.2.1.76 6.2.1.-]
103058185  [KO:K03334] [EC:1.4.3.2]
103058375  ECHS1; enoyl-CoA hydratase, mitochondrial [KO:K07511] [EC:4.2.1.17]
103058600  HIBCH; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial [KO:K05605] [EC:3.1.2.4]
103058970  [KO:K00020] [EC:1.1.1.31]
103059274  ACADM; medium-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00249] [EC:1.3.8.7]
103059584  ACADS; short-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00248] [EC:1.3.8.1]
103060614  AGXT2; alanine--glyoxylate aminotransferase 2, mitochondrial [KO:K00827] [EC:2.6.1.44 2.6.1.40]
103060849  DLD; dihydrolipoyl dehydrogenase, mitochondrial [KO:K00382] [EC:1.8.1.4]
103061299  BCKDHB; 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial [KO:K00167] [EC:1.2.4.4]
103061734  ALDH3A2; fatty aldehyde dehydrogenase isoform X2 [KO:K00128] [EC:1.2.1.3]
103062678  MCCC2; methylcrotonoyl-CoA carboxylase beta chain, mitochondrial [KO:K01969] [EC:6.4.1.4]
103063023  ACAD8; isobutyryl-CoA dehydrogenase, mitochondrial [KO:K11538] [EC:1.3.99.-]
103063101  [KO:K00020] [EC:1.1.1.31]
103063619  [KO:K00826] [EC:2.6.1.42]
103064150  [KO:K00826] [EC:2.6.1.42]
103064897  HADH; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial [KO:K00022] [EC:1.1.1.35]
103065096  MUT; methylmalonyl-CoA mutase, mitochondrial [KO:K01847] [EC:5.4.99.2]
103065639  MCCC1; methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial [KO:K01968] [EC:6.4.1.4]
103066261  ACADSB; short/branched chain specific acyl-CoA dehydrogenase, mitochondrial isoform X1 [KO:K09478] [EC:1.3.8.5]
103067001  AUH; methylglutaconyl-CoA hydratase, mitochondrial [KO:K05607] [EC:4.2.1.18]
103067464  HMGCL; hydroxymethylglutaryl-CoA lyase, mitochondrial isoform X2 [KO:K01640] [EC:4.1.3.4]
103067641  ACAT1; acetyl-CoA acetyltransferase, mitochondrial [KO:K00626] [EC:2.3.1.9]
103067794  [KO:K01907] [EC:6.2.1.16]
Compound
C00024  Acetyl-CoA
C00068  Thiamin diphosphate
C00091  Succinyl-CoA
C00100  Propanoyl-CoA
C00123  L-Leucine
C00141  3-Methyl-2-oxobutanoic acid
C00164  Acetoacetate
C00183  L-Valine
C00233  4-Methyl-2-oxopentanoate
C00332  Acetoacetyl-CoA
C00349  2-Methyl-3-oxopropanoate
C00356  (S)-3-Hydroxy-3-methylglutaryl-CoA
C00407  L-Isoleucine
C00630  2-Methylpropanoyl-CoA
C00671  (S)-3-Methyl-2-oxopentanoic acid
C00683  (S)-Methylmalonyl-CoA
C01205  (R)-3-Amino-2-methylpropanoate
C01213  (R)-Methylmalonyl-CoA
C02170  Methylmalonate
C02939  3-Methylbutanoyl-CoA
C03069  3-Methylcrotonyl-CoA
C03231  3-Methylglutaconyl-CoA
C03284  L-3-Aminoisobutanoate
C03344  2-Methylacetoacetyl-CoA
C03345  2-Methylbut-2-enoyl-CoA
C03460  2-Methylprop-2-enoyl-CoA
C04405  (2S,3S)-3-Hydroxy-2-methylbutanoyl-CoA
C05996  Branched chain fatty acid
C05998  3-Hydroxyisovaleryl-CoA
C06000  (S)-3-Hydroxyisobutyryl-CoA
C06001  (S)-3-Hydroxyisobutyrate
C06002  (S)-Methylmalonate semialdehyde
C15972  Enzyme N6-(lipoyl)lysine
C15973  Enzyme N6-(dihydrolipoyl)lysine
C15974  3-Methyl-1-hydroxybutyl-ThPP
C15975  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(3-methylbutanoyl)dihydrolipoyllysine
C15976  2-Methyl-1-hydroxypropyl-ThPP
C15977  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine
C15978  2-Methyl-1-hydroxybutyl-ThPP
C15979  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylbutanoyl)dihydrolipoyllysine
C15980  (S)-2-Methylbutanoyl-CoA
C20827  3-Hydroxyisovalerate
Related
pathway
pbi00020  Citrate cycle (TCA cycle)
pbi00240  Pyrimidine metabolism
pbi00290  Valine, leucine and isoleucine biosynthesis
pbi00640  Propanoate metabolism
pbi00900  Terpenoid backbone biosynthesis
KO pathway
ko00280   

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