KEGG   PATHWAY: sgh00280
Entry
sgh00280                    Pathway                                
Name
Valine, leucine and isoleucine degradation - Sinocyclocheilus grahami (golden-line barbel)
Class
Metabolism; Amino acid metabolism
Pathway map
sgh00280  Valine, leucine and isoleucine degradation
sgh00280

Module
sgh_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA [PATH:sgh00280]
sgh_M00741  Propanoyl-CoA metabolism, propanoyl-CoA => succinyl-CoA [PATH:sgh00280]
Other DBs
GO: 0006550 0006552 0006574
Organism
Sinocyclocheilus grahami (golden-line barbel) [GN:sgh]
Gene
107548528  aldh2; aldehyde dehydrogenase, mitochondrial [KO:K00128] [EC:1.2.1.3]
107549103  aldh9a1; 4-trimethylaminobutyraldehyde dehydrogenase [KO:K00149] [EC:1.2.1.47 1.2.1.3]
107549121  [KO:K00626] [EC:2.3.1.9]
107550361  [KO:K07515] [EC:4.2.1.17 1.1.1.211]
107550362  [KO:K07509] [EC:2.3.1.16]
107550605  pccb; propionyl-CoA carboxylase beta chain, mitochondrial isoform X1 [KO:K01966] [EC:6.4.1.3 2.1.3.15]
107550829  [KO:K00020] [EC:1.1.1.31]
107551165  [KO:K00826] [EC:2.6.1.42]
107552565  [KO:K01969] [EC:6.4.1.4]
107552936  echs1; enoyl-CoA hydratase, mitochondrial [KO:K07511] [EC:4.2.1.17]
107553609  [KO:K01969] [EC:6.4.1.4]
107554504  [KO:K00166] [EC:1.2.4.4]
107558265  auh; methylglutaconyl-CoA hydratase, mitochondrial isoform X1 [KO:K05607] [EC:4.2.1.18]
107559046  [KO:K00167] [EC:1.2.4.4]
107559599  acaa2; 3-ketoacyl-CoA thiolase, mitochondrial [KO:K07508] [EC:2.3.1.16]
107559872  [KO:K00140] [EC:1.2.1.18 1.2.1.27]
107560150  [KO:K00166] [EC:1.2.4.4]
107560905  [KO:K08683] [EC:1.1.1.35 1.1.1.178]
107561362  [KO:K00826] [EC:2.6.1.42]
107561460  [KO:K18660] [EC:6.2.1.76 6.2.1.-]
107562460  [KO:K08683] [EC:1.1.1.35 1.1.1.178]
107563384  ivd; isovaleryl-CoA dehydrogenase, mitochondrial [KO:K00253] [EC:1.3.8.4]
107565011  hibch; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial isoform X1 [KO:K05605] [EC:3.1.2.4]
107565056  [KO:K01640] [EC:4.1.3.4]
107565255  [KO:K00626] [EC:2.3.1.9]
107566872  [KO:K01968] [EC:6.4.1.4]
107567748  [KO:K00248] [EC:1.3.8.1]
107568422  [KO:K13524] [EC:2.6.1.19 2.6.1.22]
107568653  hmgcs1; hydroxymethylglutaryl-CoA synthase, cytoplasmic isoform X1 [KO:K01641] [EC:2.3.3.10]
107569448  [KO:K00167] [EC:1.2.4.4]
107573911  aldh7a1; alpha-aminoadipic semialdehyde dehydrogenase [KO:K14085] [EC:1.2.1.31 1.2.1.8 1.2.1.3]
107574492  [KO:K09478] [EC:1.3.8.5]
107575708  [KO:K00382] [EC:1.8.1.4]
107576177  [KO:K07513] [EC:2.3.1.16]
107576250  [KO:K00382] [EC:1.8.1.4]
107580754  [KO:K09478] [EC:1.3.8.5]
107581929  [KO:K00128] [EC:1.2.1.3]
107582571  [KO:K11538] [EC:1.3.99.-]
107583027  [KO:K00128] [EC:1.2.1.3]
107583121  [KO:K01640] [EC:4.1.3.4]
107583243  hadh; LOW QUALITY PROTEIN: hydroxyacyl-coenzyme A dehydrogenase, mitochondrial [KO:K00022] [EC:1.1.1.35]
107583377  [KO:K00626] [EC:2.3.1.9]
107583590  [KO:K01640] [EC:4.1.3.4]
107584839  [KO:K00249] [EC:1.3.8.7]
107585917  [KO:K00149] [EC:1.2.1.47 1.2.1.3]
107585993  [KO:K05606] [EC:5.1.99.1]
107586043  [KO:K01966] [EC:6.4.1.3 2.1.3.15]
107586255  [KO:K00128] [EC:1.2.1.3]
107586302  [KO:K03334] [EC:1.4.3.2]
107586880  [KO:K00140] [EC:1.2.1.18 1.2.1.27]
107587226  [KO:K00128] [EC:1.2.1.3]
107587341  [KO:K00826] [EC:2.6.1.42]
107588055  [KO:K09699] [EC:2.3.1.168]
107588820  pcca; LOW QUALITY PROTEIN: propionyl-CoA carboxylase alpha chain, mitochondrial [KO:K01965] [EC:6.4.1.3]
107589029  [KO:K00248] [EC:1.3.8.1]
107589277  oxct1; succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial [KO:K01027] [EC:2.8.3.5]
107590116  [KO:K00826] [EC:2.6.1.42]
107590587  abat; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
107591283  [KO:K07513] [EC:2.3.1.16]
107591691  [KO:K01027] [EC:2.8.3.5]
107592003  [KO:K00020] [EC:1.1.1.31]
107592709  [KO:K09699] [EC:2.3.1.168]
107593272  [KO:K07515] [EC:4.2.1.17 1.1.1.211]
107593292  [KO:K07509] [EC:2.3.1.16]
107593789  [KO:K00149] [EC:1.2.1.47 1.2.1.3]
107593857  [KO:K09699] [EC:2.3.1.168]
107594428  [KO:K00022] [EC:1.1.1.35]
107594700  [KO:K07515] [EC:4.2.1.17 1.1.1.211]
107594842  [KO:K00253] [EC:1.3.8.4]
107595079  [KO:K05606] [EC:5.1.99.1]
107595953  [KO:K01907] [EC:6.2.1.16]
107596516  [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
107596727  [KO:K00020] [EC:1.1.1.31]
107597304  aacs; acetoacetyl-CoA synthetase [KO:K01907] [EC:6.2.1.16]
107597555  [KO:K00128] [EC:1.2.1.3]
107597574  [KO:K11538] [EC:1.3.99.-]
107597721  hmgcll1; 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic [KO:K01640] [EC:4.1.3.4]
107598889  [KO:K00382] [EC:1.8.1.4]
107599801  [KO:K01969] [EC:6.4.1.4]
107600019  [KO:K01027] [EC:2.8.3.5]
107600108  [KO:K01847] [EC:5.4.99.2]
107600864  [KO:K07515] [EC:4.2.1.17 1.1.1.211]
107600890  [KO:K00827] [EC:2.6.1.44 2.6.1.40]
107600982  [KO:K00157] [EC:1.2.3.1]
107600984  [KO:K00157] [EC:1.2.3.1]
107601581  [KO:K00626] [EC:2.3.1.9]
107601700  [KO:K03334] [EC:1.4.3.2]
107601864  [KO:K07511] [EC:4.2.1.17]
107602132  [KO:K05605] [EC:3.1.2.4]
107602396  [KO:K00020] [EC:1.1.1.31]
107602542  [KO:K00249] [EC:1.3.8.7]
107602870  [KO:K01027] [EC:2.8.3.5]
107603104  mut; methylmalonyl-CoA mutase, mitochondrial [KO:K01847] [EC:5.4.99.2]
Compound
C00024  Acetyl-CoA
C00068  Thiamin diphosphate
C00091  Succinyl-CoA
C00100  Propanoyl-CoA
C00123  L-Leucine
C00141  3-Methyl-2-oxobutanoic acid
C00164  Acetoacetate
C00183  L-Valine
C00233  4-Methyl-2-oxopentanoate
C00332  Acetoacetyl-CoA
C00349  2-Methyl-3-oxopropanoate
C00356  (S)-3-Hydroxy-3-methylglutaryl-CoA
C00407  L-Isoleucine
C00630  2-Methylpropanoyl-CoA
C00671  (S)-3-Methyl-2-oxopentanoic acid
C00683  (S)-Methylmalonyl-CoA
C01205  (R)-3-Amino-2-methylpropanoate
C01213  (R)-Methylmalonyl-CoA
C02170  Methylmalonate
C02939  3-Methylbutanoyl-CoA
C03069  3-Methylcrotonyl-CoA
C03231  3-Methylglutaconyl-CoA
C03284  L-3-Aminoisobutanoate
C03344  2-Methylacetoacetyl-CoA
C03345  2-Methylbut-2-enoyl-CoA
C03460  2-Methylprop-2-enoyl-CoA
C04405  (2S,3S)-3-Hydroxy-2-methylbutanoyl-CoA
C05996  Branched chain fatty acid
C05998  3-Hydroxyisovaleryl-CoA
C06000  (S)-3-Hydroxyisobutyryl-CoA
C06001  (S)-3-Hydroxyisobutyrate
C06002  (S)-Methylmalonate semialdehyde
C15972  Enzyme N6-(lipoyl)lysine
C15973  Enzyme N6-(dihydrolipoyl)lysine
C15974  3-Methyl-1-hydroxybutyl-ThPP
C15975  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(3-methylbutanoyl)dihydrolipoyllysine
C15976  2-Methyl-1-hydroxypropyl-ThPP
C15977  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine
C15978  2-Methyl-1-hydroxybutyl-ThPP
C15979  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylbutanoyl)dihydrolipoyllysine
C15980  (S)-2-Methylbutanoyl-CoA
C20827  3-Hydroxyisovalerate
Related
pathway
sgh00020  Citrate cycle (TCA cycle)
sgh00240  Pyrimidine metabolism
sgh00290  Valine, leucine and isoleucine biosynthesis
sgh00640  Propanoate metabolism
sgh00900  Terpenoid backbone biosynthesis
KO pathway
ko00280   

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