KEGG   PATHWAY: amj00280
Entry
amj00280                    Pathway                                
Name
Valine, leucine and isoleucine degradation - Alligator mississippiensis (American alligator)
Class
Metabolism; Amino acid metabolism
Pathway map
amj00280  Valine, leucine and isoleucine degradation
amj00280

Module
amj_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA [PATH:amj00280]
amj_M00741  Propanoyl-CoA metabolism, propanoyl-CoA => succinyl-CoA [PATH:amj00280]
Other DBs
GO: 0006550 0006552 0006574
Organism
Alligator mississippiensis (American alligator) [GN:amj]
Gene
102565773  BCAT2; branched chain amino acid transaminase 2 [KO:K00826] [EC:2.6.1.42]
102570565  BCAT1; branched chain amino acid transaminase 1 [KO:K00826] [EC:2.6.1.42]
102573609  IL4I1; L-amino-acid oxidase [KO:K03334] [EC:1.4.3.2]
102565465  L-amino-acid oxidase [KO:K03334] [EC:1.4.3.2]
102576924  BCKDHA; branched chain keto acid dehydrogenase E1, alpha polypeptide [KO:K00166] [EC:1.2.4.4]
102573276  BCKDHB; branched chain keto acid dehydrogenase E1 subunit beta [KO:K00167] [EC:1.2.4.4]
102560886  DBT; dihydrolipoamide branched chain transacylase E2 [KO:K09699] [EC:2.3.1.168]
102568552  DLD; dihydrolipoamide dehydrogenase [KO:K00382] [EC:1.8.1.4]
102559145  ACADS; acyl-CoA dehydrogenase, C-2 to C-3 short chain [KO:K00248] [EC:1.3.8.1]
102576335  ACADM; acyl-CoA dehydrogenase, C-4 to C-12 straight chain [KO:K00249] [EC:1.3.8.7]
102557682  IVD; isovaleryl-CoA dehydrogenase [KO:K00253] [EC:1.3.8.4]
102577069  ACADSB; acyl-CoA dehydrogenase, short/branched chain [KO:K09478] [EC:1.3.8.5]
102568657  ACAD8; acyl-CoA dehydrogenase family member 8 [KO:K11538] [EC:1.3.99.-]
102559143  HADHA; hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit [KO:K07515] [EC:4.2.1.17 1.1.1.211]
102558567  EHHADH; enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
102559204  ECHS1; enoyl-CoA hydratase, short chain 1 [KO:K07511] [EC:4.2.1.17]
102561189  HADH; hydroxyacyl-CoA dehydrogenase [KO:K00022] [EC:1.1.1.35]
102559608  HSD17B10; hydroxysteroid 17-beta dehydrogenase 10 [KO:K08683] [EC:1.1.1.35 1.1.1.178]
102562558  ACAA1; acetyl-CoA acyltransferase 1 [KO:K07513] [EC:2.3.1.16]
102568981  ACAA2; acetyl-CoA acyltransferase 2 [KO:K07508] [EC:2.3.1.16]
102559598  HADHB; hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit [KO:K07509] [EC:2.3.1.16]
102558928  PCCA; propionyl-CoA carboxylase alpha subunit [KO:K01965] [EC:6.4.1.3]
102562961  PCCB; propionyl-CoA carboxylase beta subunit [KO:K01966] [EC:6.4.1.3 2.1.3.15]
102565803  MCEE; methylmalonyl-CoA epimerase [KO:K05606] [EC:5.1.99.1]
102566480  MUT; methylmalonyl-CoA mutase [KO:K01847] [EC:5.4.99.2]
102568673  HIBCH; 3-hydroxyisobutyryl-CoA hydrolase [KO:K05605] [EC:3.1.2.4]
102572348  HIBADH; 3-hydroxyisobutyrate dehydrogenase [KO:K00020] [EC:1.1.1.31]
102566069  ALDH6A1; aldehyde dehydrogenase 6 family member A1 [KO:K00140] [EC:1.2.1.18 1.2.1.27]
102575096  ALDH16A1; aldehyde dehydrogenase 16 family member A1 [KO:K00128] [EC:1.2.1.3]
106736721  ALDH2; aldehyde dehydrogenase 2 family (mitochondrial) [KO:K00128] [EC:1.2.1.3]
102567377  ALDH3A2; aldehyde dehydrogenase 3 family member A2 [KO:K00128] [EC:1.2.1.3]
102563610  ALDH7A1; aldehyde dehydrogenase 7 family member A1 [KO:K14085] [EC:1.2.1.31 1.2.1.8 1.2.1.3]
102576324  ALDH9A1; aldehyde dehydrogenase 9 family member A1 [KO:K00149] [EC:1.2.1.47 1.2.1.3]
102558513  AOX1; aldehyde oxidase [KO:K00157] [EC:1.2.3.1]
102557817  aldehyde oxidase 2 [KO:K00157] [EC:1.2.3.1]
102558282  aldehyde oxidase [KO:K00157] [EC:1.2.3.1]
102558050  aldehyde oxidase [KO:K00157] [EC:1.2.3.1]
102560749  ACSF3; acyl-CoA synthetase family member 3 [KO:K18660] [EC:6.2.1.76 6.2.1.-]
102565561  ABAT; 4-aminobutyrate aminotransferase [KO:K13524] [EC:2.6.1.19 2.6.1.22]
102559340  AGXT2; alanine--glyoxylate aminotransferase 2 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
102565428  MCCC1; methylcrotonoyl-CoA carboxylase 1 [KO:K01968] [EC:6.4.1.4]
102572153  MCCC2; methylcrotonoyl-CoA carboxylase 2 [KO:K01969] [EC:6.4.1.4]
102560270  methylcrotonoyl-CoA carboxylase beta chain, mitochondrial [KO:K01969] [EC:6.4.1.4]
102566766  AUH; AU RNA binding methylglutaconyl-CoA hydratase [KO:K05607] [EC:4.2.1.18]
102572562  HMGCL; 3-hydroxymethyl-3-methylglutaryl-CoA lyase [KO:K01640] [EC:4.1.3.4]
102576978  HMGCLL1; 3-hydroxymethyl-3-methylglutaryl-CoA lyase like 1 [KO:K01640] [EC:4.1.3.4]
102564628  OXCT1; 3-oxoacid CoA-transferase 1 [KO:K01027] [EC:2.8.3.5]
102564646  AACS; acetoacetyl-CoA synthetase [KO:K01907] [EC:6.2.1.16]
102569153  ACAT1; acetyl-CoA acetyltransferase 1 [KO:K00626] [EC:2.3.1.9]
102565044  ACAT2; acetyl-CoA acetyltransferase 2 [KO:K00626] [EC:2.3.1.9]
106737192  HMGCS2; 3-hydroxy-3-methylglutaryl-CoA synthase 2 [KO:K01641] [EC:2.3.3.10]
102561891  HMGCS1; 3-hydroxy-3-methylglutaryl-CoA synthase 1 [KO:K01641] [EC:2.3.3.10]
Compound
C00024  Acetyl-CoA
C00068  Thiamin diphosphate
C00091  Succinyl-CoA
C00100  Propanoyl-CoA
C00123  L-Leucine
C00141  3-Methyl-2-oxobutanoic acid
C00164  Acetoacetate
C00183  L-Valine
C00233  4-Methyl-2-oxopentanoate
C00332  Acetoacetyl-CoA
C00349  2-Methyl-3-oxopropanoate
C00356  (S)-3-Hydroxy-3-methylglutaryl-CoA
C00407  L-Isoleucine
C00630  2-Methylpropanoyl-CoA
C00671  (S)-3-Methyl-2-oxopentanoic acid
C00683  (S)-Methylmalonyl-CoA
C01205  (R)-3-Amino-2-methylpropanoate
C01213  (R)-Methylmalonyl-CoA
C02170  Methylmalonate
C02939  3-Methylbutanoyl-CoA
C03069  3-Methylcrotonyl-CoA
C03231  3-Methylglutaconyl-CoA
C03284  L-3-Aminoisobutanoate
C03344  2-Methylacetoacetyl-CoA
C03345  2-Methylbut-2-enoyl-CoA
C03460  2-Methylprop-2-enoyl-CoA
C04405  (2S,3S)-3-Hydroxy-2-methylbutanoyl-CoA
C05996  Branched chain fatty acid
C05998  3-Hydroxyisovaleryl-CoA
C06000  (S)-3-Hydroxyisobutyryl-CoA
C06001  (S)-3-Hydroxyisobutyrate
C06002  (S)-Methylmalonate semialdehyde
C15972  Enzyme N6-(lipoyl)lysine
C15973  Enzyme N6-(dihydrolipoyl)lysine
C15974  3-Methyl-1-hydroxybutyl-ThPP
C15975  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(3-methylbutanoyl)dihydrolipoyllysine
C15976  2-Methyl-1-hydroxypropyl-ThPP
C15977  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine
C15978  2-Methyl-1-hydroxybutyl-ThPP
C15979  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylbutanoyl)dihydrolipoyllysine
C15980  (S)-2-Methylbutanoyl-CoA
C20827  3-Hydroxyisovalerate
Related
pathway
amj00020  Citrate cycle (TCA cycle)
amj00240  Pyrimidine metabolism
amj00290  Valine, leucine and isoleucine biosynthesis
amj00640  Propanoate metabolism
amj00900  Terpenoid backbone biosynthesis
KO pathway
ko00280   
LinkDB

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