KEGG   PATHWAY: hgl00280
Entry
hgl00280                    Pathway                                
Name
Valine, leucine and isoleucine degradation - Heterocephalus glaber (naked mole-rat)
Class
Metabolism; Amino acid metabolism
Pathway map
hgl00280  Valine, leucine and isoleucine degradation
hgl00280

Module
hgl_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA [PATH:hgl00280]
hgl_M00741  Propanoyl-CoA metabolism, propanoyl-CoA => succinyl-CoA [PATH:hgl00280]
Other DBs
GO: 0006550 0006552 0006574
Organism
Heterocephalus glaber (naked mole-rat) [GN:hgl]
Gene
101720534  Bcat1; branched chain amino acid transaminase 1 [KO:K00826] [EC:2.6.1.42]
101716132  Bcat2; branched chain amino acid transaminase 2 [KO:K00826] [EC:2.6.1.42]
101710424  Il4i1; interleukin 4 induced 1 [KO:K03334] [EC:1.4.3.2]
101705928  Bckdha; branched chain keto acid dehydrogenase E1, alpha polypeptide [KO:K00166] [EC:1.2.4.4]
101725476  Bckdhb; branched chain keto acid dehydrogenase E1 subunit beta [KO:K00167] [EC:1.2.4.4]
101722423  Dbt; dihydrolipoamide branched chain transacylase E2 [KO:K09699] [EC:2.3.1.168]
101699518  Dld; dihydrolipoamide dehydrogenase [KO:K00382] [EC:1.8.1.4]
101722158  Acads; acyl-CoA dehydrogenase, C-2 to C-3 short chain [KO:K00248] [EC:1.3.8.1]
101710282  Acadm; acyl-CoA dehydrogenase, C-4 to C-12 straight chain [KO:K00249] [EC:1.3.8.7]
101710885  Ivd; isovaleryl-CoA dehydrogenase [KO:K00253] [EC:1.3.8.4]
101698912  Acadsb; acyl-CoA dehydrogenase, short/branched chain [KO:K09478] [EC:1.3.8.5]
101709235  Acad8; acyl-CoA dehydrogenase family member 8 [KO:K11538] [EC:1.3.99.-]
101724137  Hadha; hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit [KO:K07515] [EC:4.2.1.17 1.1.1.211]
101699730  Ehhadh; enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
101697414  Echs1; enoyl-CoA hydratase, short chain 1 [KO:K07511] [EC:4.2.1.17]
101712136  Hadh; hydroxyacyl-CoA dehydrogenase [KO:K00022] [EC:1.1.1.35]
101712281  Hsd17b10; hydroxysteroid 17-beta dehydrogenase 10 [KO:K08683] [EC:1.1.1.35 1.1.1.178]
101713505  Acaa1; acetyl-CoA acyltransferase 1 [KO:K07513] [EC:2.3.1.16]
101714191  3-ketoacyl-CoA thiolase B, peroxisomal [KO:K07513] [EC:2.3.1.16]
101721744  Acaa2; acetyl-CoA acyltransferase 2 [KO:K07508] [EC:2.3.1.16]
101725212  Hadhb; hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit [KO:K07509] [EC:2.3.1.16]
101711474  Pcca; propionyl-CoA carboxylase alpha subunit [KO:K01965] [EC:6.4.1.3]
101699369  Pccb; propionyl-CoA carboxylase beta subunit [KO:K01966] [EC:6.4.1.3 2.1.3.15]
101724683  Mcee; methylmalonyl-CoA epimerase [KO:K05606] [EC:5.1.99.1]
101726092  Mut; methylmalonyl-CoA mutase [KO:K01847] [EC:5.4.99.2]
101725904  Hibch; 3-hydroxyisobutyryl-CoA hydrolase [KO:K05605] [EC:3.1.2.4]
101705721  Hibadh; 3-hydroxyisobutyrate dehydrogenase [KO:K00020] [EC:1.1.1.31]
101705709  Aldh6a1; aldehyde dehydrogenase 6 family member A1 [KO:K00140] [EC:1.2.1.18 1.2.1.27]
101706449  Aldh2; aldehyde dehydrogenase 2 family (mitochondrial) [KO:K00128] [EC:1.2.1.3]
101711406  Aldh3a2; aldehyde dehydrogenase 3 family member A2 [KO:K00128] [EC:1.2.1.3]
101701236  Aldh1b1; aldehyde dehydrogenase 1 family member B1 [KO:K00128] [EC:1.2.1.3]
101700529  Aldh16a1; aldehyde dehydrogenase 16 family member A1 [KO:K00128] [EC:1.2.1.3]
101711696  Aldh7a1; aldehyde dehydrogenase 7 family member A1 [KO:K14085] [EC:1.2.1.31 1.2.1.8 1.2.1.3]
101717741  Aldh9a1; aldehyde dehydrogenase 9 family member A1 [KO:K00149] [EC:1.2.1.47 1.2.1.3]
101710340  aldehyde oxidase 2-like [KO:K00157] [EC:1.2.3.1]
101722324  Aox4; aldehyde oxidase-like [KO:K00157] [EC:1.2.3.1]
101722898  Aox1; aldehyde oxidase 1 [KO:K00157] [EC:1.2.3.1]
101708737  Acsf3; acyl-CoA synthetase family member 3 [KO:K18660] [EC:6.2.1.76 6.2.1.-]
101712584  Abat; 4-aminobutyrate aminotransferase [KO:K13524] [EC:2.6.1.19 2.6.1.22]
101714498  Agxt2; alanine--glyoxylate aminotransferase 2 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
101704843  Mccc1; methylcrotonoyl-CoA carboxylase 1 [KO:K01968] [EC:6.4.1.4]
101709282  Mccc2; methylcrotonoyl-CoA carboxylase 2 [KO:K01969] [EC:6.4.1.4]
101719138  Auh; AU RNA binding methylglutaconyl-CoA hydratase [KO:K05607] [EC:4.2.1.18]
101716848  Hmgcl; 3-hydroxymethyl-3-methylglutaryl-CoA lyase [KO:K01640] [EC:4.1.3.4]
101723463  Hmgcll1; 3-hydroxymethyl-3-methylglutaryl-CoA lyase like 1 [KO:K01640] [EC:4.1.3.4]
101718900  Oxct1; 3-oxoacid CoA-transferase 1 [KO:K01027] [EC:2.8.3.5]
101716155  Oxct2; 3-oxoacid CoA-transferase 2 [KO:K01027] [EC:2.8.3.5]
101700737  Aacs; acetoacetyl-CoA synthetase [KO:K01907] [EC:6.2.1.16]
101709659  Acat1; acetyl-CoA acetyltransferase 1 [KO:K00626] [EC:2.3.1.9]
101712256  Acat2; acetyl-CoA acetyltransferase 2 [KO:K00626] [EC:2.3.1.9]
101712604  Hmgcs1; 3-hydroxy-3-methylglutaryl-CoA synthase 1 [KO:K01641] [EC:2.3.3.10]
101712063  Hmgcs2; 3-hydroxy-3-methylglutaryl-CoA synthase 2 [KO:K01641] [EC:2.3.3.10]
Compound
C00024  Acetyl-CoA
C00068  Thiamin diphosphate
C00091  Succinyl-CoA
C00100  Propanoyl-CoA
C00123  L-Leucine
C00141  3-Methyl-2-oxobutanoic acid
C00164  Acetoacetate
C00183  L-Valine
C00233  4-Methyl-2-oxopentanoate
C00332  Acetoacetyl-CoA
C00349  2-Methyl-3-oxopropanoate
C00356  (S)-3-Hydroxy-3-methylglutaryl-CoA
C00407  L-Isoleucine
C00630  2-Methylpropanoyl-CoA
C00671  (S)-3-Methyl-2-oxopentanoic acid
C00683  (S)-Methylmalonyl-CoA
C01205  (R)-3-Amino-2-methylpropanoate
C01213  (R)-Methylmalonyl-CoA
C02170  Methylmalonate
C02939  3-Methylbutanoyl-CoA
C03069  3-Methylcrotonyl-CoA
C03231  3-Methylglutaconyl-CoA
C03284  L-3-Aminoisobutanoate
C03344  2-Methylacetoacetyl-CoA
C03345  2-Methylbut-2-enoyl-CoA
C03460  2-Methylprop-2-enoyl-CoA
C04405  (2S,3S)-3-Hydroxy-2-methylbutanoyl-CoA
C05996  Branched chain fatty acid
C05998  3-Hydroxyisovaleryl-CoA
C06000  (S)-3-Hydroxyisobutyryl-CoA
C06001  (S)-3-Hydroxyisobutyrate
C06002  (S)-Methylmalonate semialdehyde
C15972  Enzyme N6-(lipoyl)lysine
C15973  Enzyme N6-(dihydrolipoyl)lysine
C15974  3-Methyl-1-hydroxybutyl-ThPP
C15975  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(3-methylbutanoyl)dihydrolipoyllysine
C15976  2-Methyl-1-hydroxypropyl-ThPP
C15977  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine
C15978  2-Methyl-1-hydroxybutyl-ThPP
C15979  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylbutanoyl)dihydrolipoyllysine
C15980  (S)-2-Methylbutanoyl-CoA
C20827  3-Hydroxyisovalerate
Related
pathway
hgl00020  Citrate cycle (TCA cycle)
hgl00240  Pyrimidine metabolism
hgl00290  Valine, leucine and isoleucine biosynthesis
hgl00640  Propanoate metabolism
hgl00900  Terpenoid backbone biosynthesis
KO pathway
ko00280   
LinkDB

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