KEGG   PATHWAY: pleu00280
Entry
pleu00280                   Pathway                                
Name
Valine, leucine and isoleucine degradation - Peromyscus leucopus (white-footed mouse)
Class
Metabolism; Amino acid metabolism
Pathway map
pleu00280  Valine, leucine and isoleucine degradation
pleu00280

Module
pleu_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA [PATH:pleu00280]
pleu_M00741  Propanoyl-CoA metabolism, propanoyl-CoA => succinyl-CoA [PATH:pleu00280]
Other DBs
GO: 0006550 0006552 0006574
Organism
Peromyscus leucopus (white-footed mouse) [GN:pleu]
Gene
114684687  Bcat2; branched-chain-amino-acid aminotransferase, mitochondrial isoform X2 [KO:K00826] [EC:2.6.1.42]
114708468  Bcat1; branched-chain-amino-acid aminotransferase, cytosolic isoform X1 [KO:K00826] [EC:2.6.1.42]
114684326  Il4i1; L-amino-acid oxidase isoform X1 [KO:K03334] [EC:1.4.3.2]
114686459  L-amino-acid oxidase-like isoform X1 [KO:K03334] [EC:1.4.3.2]
114704946  L-amino-acid oxidase-like [KO:K03334] [EC:1.4.3.2]
114685294  Bckdha; 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial isoform X1 [KO:K00166] [EC:1.2.4.4]
114697279  Bckdhb; 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X2 [KO:K00167] [EC:1.2.4.4]
114707415  Dbt; lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial isoform X1 [KO:K09699] [EC:2.3.1.168]
114708456  Dld; dihydrolipoyl dehydrogenase, mitochondrial [KO:K00382] [EC:1.8.1.4]
114681328  Acads; short-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00248] [EC:1.3.8.1]
114699854  Acadm; medium-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00249] [EC:1.3.8.7]
114704637  Ivd; isovaleryl-CoA dehydrogenase, mitochondrial [KO:K00253] [EC:1.3.8.4]
114692584  Acadsb; short/branched chain specific acyl-CoA dehydrogenase, mitochondrial isoform X1 [KO:K09478] [EC:1.3.8.5]
114702585  Acad8; isobutyryl-CoA dehydrogenase, mitochondrial isoform X1 [KO:K11538] [EC:1.3.99.-]
114696488  Hadha; trifunctional enzyme subunit alpha, mitochondrial [KO:K07515] [EC:4.2.1.17 1.1.1.211]
114684255  Ehhadh; peroxisomal bifunctional enzyme [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
114684664  LOW QUALITY PROTEIN: peroxisomal bifunctional enzyme-like [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
114687893  peroxisomal bifunctional enzyme [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
114693360  Echs1; enoyl-CoA hydratase, mitochondrial [KO:K07511] [EC:4.2.1.17]
114682849  Hadh; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial [KO:K00022] [EC:1.1.1.35]
114683399  3-hydroxyacyl-CoA dehydrogenase type-2 [KO:K08683] [EC:1.1.1.35 1.1.1.178]
114702840  Hsd17b10; LOW QUALITY PROTEIN: 3-hydroxyacyl-CoA dehydrogenase type-2 [KO:K08683] [EC:1.1.1.35 1.1.1.178]
114682502  LOW QUALITY PROTEIN: 3-ketoacyl-CoA thiolase B, peroxisomal-like [KO:K07513] [EC:2.3.1.16]
114682509  3-ketoacyl-CoA thiolase B, peroxisomal [KO:K07513] [EC:2.3.1.16]
114694872  Acaa2; 3-ketoacyl-CoA thiolase, mitochondrial [KO:K07508] [EC:2.3.1.16]
114688599  LOW QUALITY PROTEIN: trifunctional enzyme subunit beta, mitochondrial-like [KO:K07509] [EC:2.3.1.16]
114696496  Hadhb; trifunctional enzyme subunit beta, mitochondrial [KO:K07509] [EC:2.3.1.16]
114692496  Pcca; propionyl-CoA carboxylase alpha chain, mitochondrial [KO:K01965] [EC:6.4.1.3]
114693544  Pccb; LOW QUALITY PROTEIN: propionyl-CoA carboxylase beta chain, mitochondrial [KO:K01966] [EC:6.4.1.3 2.1.3.15]
114695494  Mcee; methylmalonyl-CoA epimerase, mitochondrial [KO:K05606] [EC:5.1.99.1]
114705383  Mmut; methylmalonyl-CoA mutase, mitochondrial [KO:K01847] [EC:5.4.99.2]
114705116  Hibch; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial isoform X1 [KO:K05605] [EC:3.1.2.4]
114689730  Hibadh; 3-hydroxyisobutyrate dehydrogenase, mitochondrial [KO:K00020] [EC:1.1.1.31]
114707455  3-hydroxyisobutyrate dehydrogenase, mitochondrial-like [KO:K00020] [EC:1.1.1.31]
114698244  Aldh6a1; methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial [KO:K00140] [EC:1.2.1.18 1.2.1.27]
114683273  Aldh3a2; aldehyde dehydrogenase family 3 member A2 isoform X1 [KO:K00128] [EC:1.2.1.3]
114684962  Aldh1b1; aldehyde dehydrogenase X, mitochondrial [KO:K00128] [EC:1.2.1.3]
114687173  Aldh16a1; aldehyde dehydrogenase family 16 member A1 [KO:K00128] [EC:1.2.1.3]
114681892  Aldh2; aldehyde dehydrogenase, mitochondrial [KO:K00128] [EC:1.2.1.3]
114706088  Aldh7a1; alpha-aminoadipic semialdehyde dehydrogenase [KO:K14085] [EC:1.2.1.31 1.2.1.8 1.2.1.3]
114689914  Aldh9a1; 4-trimethylaminobutyraldehyde dehydrogenase [KO:K00149] [EC:1.2.1.47 1.2.1.3]
114694603  4-trimethylaminobutyraldehyde dehydrogenase-like [KO:K00149] [EC:1.2.1.47 1.2.1.3]
114695271  4-trimethylaminobutyraldehyde dehydrogenase-like [KO:K00149] [EC:1.2.1.47 1.2.1.3]
114704265  aldehyde oxidase 2 [KO:K00157] [EC:1.2.3.1]
114704588  aldehyde oxidase 4 isoform X1 [KO:K00157] [EC:1.2.3.1]
114704606  aldehyde oxidase 3 isoform X1 [KO:K00157] [EC:1.2.3.1]
114704613  aldehyde oxidase 1 [KO:K00157] [EC:1.2.3.1]
114700982  Acsf3; malonate--CoA ligase ACSF3, mitochondrial isoform X1 [KO:K18660] [EC:6.2.1.76 6.2.1.-]
114695524  Abat; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
114710800  Agxt2; alanine--glyoxylate aminotransferase 2, mitochondrial isoform X1 [KO:K00827] [EC:2.6.1.44 2.6.1.40]
114684064  Mccc1; methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial isoform X2 [KO:K01968] [EC:6.4.1.4]
114694678  Mccc2; methylcrotonoyl-CoA carboxylase beta chain, mitochondrial isoform X2 [KO:K01969] [EC:6.4.1.4]
114689479  Auh; methylglutaconyl-CoA hydratase, mitochondrial isoform X1 [KO:K05607] [EC:4.2.1.18]
114690269  Hmgcll1; 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic [KO:K01640] [EC:4.1.3.4]
114697231  Hmgcl; hydroxymethylglutaryl-CoA lyase, mitochondrial [KO:K01640] [EC:4.1.3.4]
114681159  Oxct2; LOW QUALITY PROTEIN: succinyl-CoA:3-ketoacid coenzyme A transferase 2, mitochondrial [KO:K01027] [EC:2.8.3.5]
114681164  succinyl-CoA:3-ketoacid coenzyme A transferase 2A, mitochondrial-like [KO:K01027] [EC:2.8.3.5]
114697332  Oxct1; succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial [KO:K01027] [EC:2.8.3.5]
114710200  Aacs; acetoacetyl-CoA synthetase [KO:K01907] [EC:6.2.1.16]
114690279  Acat1; acetyl-CoA acetyltransferase, mitochondrial [KO:K00626] [EC:2.3.1.9]
114691377  acetyl-CoA acetyltransferase, cytosolic [KO:K00626] [EC:2.3.1.9]
114691378  acetyl-CoA acetyltransferase, cytosolic-like [KO:K00626] [EC:2.3.1.9]
114686258  hydroxymethylglutaryl-CoA synthase, mitochondrial [KO:K01641] [EC:2.3.3.10]
114688198  Hmgcs2; hydroxymethylglutaryl-CoA synthase, mitochondrial [KO:K01641] [EC:2.3.3.10]
114704248  Hmgcs1; hydroxymethylglutaryl-CoA synthase, cytoplasmic isoform X2 [KO:K01641] [EC:2.3.3.10]
114695894  LOW QUALITY PROTEIN: hydroxymethylglutaryl-CoA synthase, cytoplasmic-like [KO:K01641] [EC:2.3.3.10]
Compound
C00024  Acetyl-CoA
C00068  Thiamin diphosphate
C00091  Succinyl-CoA
C00100  Propanoyl-CoA
C00123  L-Leucine
C00141  3-Methyl-2-oxobutanoic acid
C00164  Acetoacetate
C00183  L-Valine
C00233  4-Methyl-2-oxopentanoate
C00332  Acetoacetyl-CoA
C00349  2-Methyl-3-oxopropanoate
C00356  (S)-3-Hydroxy-3-methylglutaryl-CoA
C00407  L-Isoleucine
C00630  2-Methylpropanoyl-CoA
C00671  (S)-3-Methyl-2-oxopentanoic acid
C00683  (S)-Methylmalonyl-CoA
C01205  (R)-3-Amino-2-methylpropanoate
C01213  (R)-Methylmalonyl-CoA
C02170  Methylmalonate
C02939  3-Methylbutanoyl-CoA
C03069  3-Methylcrotonyl-CoA
C03231  3-Methylglutaconyl-CoA
C03284  L-3-Aminoisobutanoate
C03344  2-Methylacetoacetyl-CoA
C03345  2-Methylbut-2-enoyl-CoA
C03460  2-Methylprop-2-enoyl-CoA
C04405  (2S,3S)-3-Hydroxy-2-methylbutanoyl-CoA
C05996  Branched chain fatty acid
C05998  3-Hydroxyisovaleryl-CoA
C06000  (S)-3-Hydroxyisobutyryl-CoA
C06001  (S)-3-Hydroxyisobutyrate
C06002  (S)-Methylmalonate semialdehyde
C15972  Enzyme N6-(lipoyl)lysine
C15973  Enzyme N6-(dihydrolipoyl)lysine
C15974  3-Methyl-1-hydroxybutyl-ThPP
C15975  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(3-methylbutanoyl)dihydrolipoyllysine
C15976  2-Methyl-1-hydroxypropyl-ThPP
C15977  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine
C15978  2-Methyl-1-hydroxybutyl-ThPP
C15979  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylbutanoyl)dihydrolipoyllysine
C15980  (S)-2-Methylbutanoyl-CoA
C20827  3-Hydroxyisovalerate
Related
pathway
pleu00020  Citrate cycle (TCA cycle)
pleu00240  Pyrimidine metabolism
pleu00290  Valine, leucine and isoleucine biosynthesis
pleu00640  Propanoate metabolism
pleu00900  Terpenoid backbone biosynthesis
KO pathway
ko00280   
LinkDB

DBGET integrated database retrieval system