KEGG   PATHWAY: mlx00280
Entry
mlx00280                    Pathway                                
Name
Valine, leucine and isoleucine degradation - Mirounga leonina (Southern elephant seal)
Class
Metabolism; Amino acid metabolism
Pathway map
mlx00280  Valine, leucine and isoleucine degradation
mlx00280

Module
mlx_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA [PATH:mlx00280]
mlx_M00741  Propanoyl-CoA metabolism, propanoyl-CoA => succinyl-CoA [PATH:mlx00280]
Other DBs
GO: 0006550 0006552 0006574
Organism
Mirounga leonina (Southern elephant seal) [GN:mlx]
Gene
117998069  ECHS1; enoyl-CoA hydratase, mitochondrial [KO:K07511] [EC:4.2.1.17]
117998235  BCAT2; branched-chain-amino-acid aminotransferase, mitochondrial [KO:K00826] [EC:2.6.1.42]
117998267  ALDH16A1; aldehyde dehydrogenase family 16 member A1 [KO:K00128] [EC:1.2.1.3]
117998280  IL4I1; L-amino-acid oxidase [KO:K03334] [EC:1.4.3.2]
117998525  HSD17B10; 3-hydroxyacyl-CoA dehydrogenase type-2 [KO:K08683] [EC:1.1.1.35 1.1.1.178]
118000124  ALDH3A2; aldehyde dehydrogenase family 3 member A2 [KO:K00128] [EC:1.2.1.3]
118000455  HMGCS2; hydroxymethylglutaryl-CoA synthase, mitochondrial [KO:K01641] [EC:2.3.3.10]
118000645  HMGCLL1; 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic [KO:K01640] [EC:4.1.3.4]
118001420  BCKDHB; 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X1 [KO:K00167] [EC:1.2.4.4]
118001434  MMUT; methylmalonyl-CoA mutase, mitochondrial isoform X1 [KO:K01847] [EC:5.4.99.2]
118001865  [KO:K00626] [EC:2.3.1.9]
118001887  [KO:K00626] [EC:2.3.1.9]
118001909  ACAA1; 3-ketoacyl-CoA thiolase, peroxisomal isoform X1 [KO:K07513] [EC:2.3.1.16]
118002656  ALDH6A1; methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial [KO:K00140] [EC:1.2.1.18 1.2.1.27]
118002973  IVD; isovaleryl-CoA dehydrogenase, mitochondrial [KO:K00253] [EC:1.3.8.4]
118004117  PCCB; propionyl-CoA carboxylase beta chain, mitochondrial isoform X1 [KO:K01966] [EC:6.4.1.3 2.1.3.15]
118004702  ACAA2; 3-ketoacyl-CoA thiolase, mitochondrial [KO:K07508] [EC:2.3.1.16]
118006359  [KO:K00827] [EC:2.6.1.44 2.6.1.40]
118006422  [KO:K01641] [EC:2.3.3.10]
118006428  [KO:K01027] [EC:2.8.3.5]
118006488  [KO:K00827] [EC:2.6.1.44 2.6.1.40]
118006560  [KO:K01027] [EC:2.8.3.5]
118006561  [KO:K01641] [EC:2.3.3.10]
118006867  MCCC1; methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial isoform X1 [KO:K01968] [EC:6.4.1.4]
118006911  EHHADH; peroxisomal bifunctional enzyme [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
118007670  HADHA; trifunctional enzyme subunit alpha, mitochondrial [KO:K07515] [EC:4.2.1.17 1.1.1.211]
118007671  HADHB; trifunctional enzyme subunit beta, mitochondrial isoform X1 [KO:K07509] [EC:2.3.1.16]
118009262  PCCA; propionyl-CoA carboxylase alpha chain, mitochondrial isoform X1 [KO:K01965] [EC:6.4.1.3]
118009943  [KO:K07509] [EC:2.3.1.16]
118010107  [KO:K00128] [EC:1.2.1.3]
118012164  [KO:K00157] [EC:1.2.3.1]
118012215  HIBCH; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial isoform X1 [KO:K05605] [EC:3.1.2.4]
118012656  [KO:K00157] [EC:1.2.3.1]
118012657  [KO:K00157] [EC:1.2.3.1]
118013185  ACAT1; acetyl-CoA acetyltransferase, mitochondrial [KO:K00626] [EC:2.3.1.9]
118013512  ACAD8; isobutyryl-CoA dehydrogenase, mitochondrial [KO:K11538] [EC:1.3.99.-]
118014052  ALDH9A1; 4-trimethylaminobutyraldehyde dehydrogenase isoform X1 [KO:K00149] [EC:1.2.1.47 1.2.1.3]
118016584  ALDH7A1; alpha-aminoadipic semialdehyde dehydrogenase [KO:K14085] [EC:1.2.1.31 1.2.1.8 1.2.1.3]
118016885  MCCC2; methylcrotonoyl-CoA carboxylase beta chain, mitochondrial [KO:K01969] [EC:6.4.1.4]
118017928  ALDH1B1; LOW QUALITY PROTEIN: aldehyde dehydrogenase X, mitochondrial [KO:K00128] [EC:1.2.1.3]
118018373  AACS; acetoacetyl-CoA synthetase isoform X1 [KO:K01907] [EC:6.2.1.16]
118018478  ALDH2; aldehyde dehydrogenase, mitochondrial [KO:K00128] [EC:1.2.1.3]
118018557  ACADS; short-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00248] [EC:1.3.8.1]
118019088  DBT; lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial [KO:K09699] [EC:2.3.1.168]
118019258  ACADM; medium-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00249] [EC:1.3.8.7]
118019531  [KO:K03334] [EC:1.4.3.2]
118019884  HMGCL; hydroxymethylglutaryl-CoA lyase, mitochondrial isoform X1 [KO:K01640] [EC:4.1.3.4]
118020610  DLD; dihydrolipoyl dehydrogenase, mitochondrial [KO:K00382] [EC:1.8.1.4]
118020908  HIBADH; 3-hydroxyisobutyrate dehydrogenase, mitochondrial [KO:K00020] [EC:1.1.1.31]
118021813  ABAT; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
118022626  BCKDHA; 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial [KO:K00166] [EC:1.2.4.4]
118022973  MCEE; methylmalonyl-CoA epimerase, mitochondrial isoform X1 [KO:K05606] [EC:5.1.99.1]
118023458  ACSF3; malonate--CoA ligase ACSF3, mitochondrial isoform X1 [KO:K18660] [EC:6.2.1.76 6.2.1.-]
118025575  BCAT1; branched-chain-amino-acid aminotransferase, cytosolic isoform X1 [KO:K00826] [EC:2.6.1.42]
118026364  AUH; methylglutaconyl-CoA hydratase, mitochondrial isoform X1 [KO:K05607] [EC:4.2.1.18]
118027078  HADH; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial isoform X1 [KO:K00022] [EC:1.1.1.35]
118027358  ACADSB; short/branched chain specific acyl-CoA dehydrogenase, mitochondrial isoform X1 [KO:K09478] [EC:1.3.8.5]
Compound
C00024  Acetyl-CoA
C00068  Thiamin diphosphate
C00091  Succinyl-CoA
C00100  Propanoyl-CoA
C00123  L-Leucine
C00141  3-Methyl-2-oxobutanoic acid
C00164  Acetoacetate
C00183  L-Valine
C00233  4-Methyl-2-oxopentanoate
C00332  Acetoacetyl-CoA
C00349  2-Methyl-3-oxopropanoate
C00356  (S)-3-Hydroxy-3-methylglutaryl-CoA
C00407  L-Isoleucine
C00630  2-Methylpropanoyl-CoA
C00671  (S)-3-Methyl-2-oxopentanoic acid
C00683  (S)-Methylmalonyl-CoA
C01205  (R)-3-Amino-2-methylpropanoate
C01213  (R)-Methylmalonyl-CoA
C02170  Methylmalonate
C02939  3-Methylbutanoyl-CoA
C03069  3-Methylcrotonyl-CoA
C03231  3-Methylglutaconyl-CoA
C03284  L-3-Aminoisobutanoate
C03344  2-Methylacetoacetyl-CoA
C03345  2-Methylbut-2-enoyl-CoA
C03460  2-Methylprop-2-enoyl-CoA
C04405  (2S,3S)-3-Hydroxy-2-methylbutanoyl-CoA
C05996  Branched chain fatty acid
C05998  3-Hydroxyisovaleryl-CoA
C06000  (S)-3-Hydroxyisobutyryl-CoA
C06001  (S)-3-Hydroxyisobutyrate
C06002  (S)-Methylmalonate semialdehyde
C15972  Enzyme N6-(lipoyl)lysine
C15973  Enzyme N6-(dihydrolipoyl)lysine
C15974  3-Methyl-1-hydroxybutyl-ThPP
C15975  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(3-methylbutanoyl)dihydrolipoyllysine
C15976  2-Methyl-1-hydroxypropyl-ThPP
C15977  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine
C15978  2-Methyl-1-hydroxybutyl-ThPP
C15979  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylbutanoyl)dihydrolipoyllysine
C15980  (S)-2-Methylbutanoyl-CoA
C20827  3-Hydroxyisovalerate
Related
pathway
mlx00020  Citrate cycle (TCA cycle)
mlx00240  Pyrimidine metabolism
mlx00290  Valine, leucine and isoleucine biosynthesis
mlx00640  Propanoate metabolism
mlx00900  Terpenoid backbone biosynthesis
KO pathway
ko00280   

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