KEGG   PATHWAY: ssc00280
Entry
ssc00280                    Pathway                                
Name
Valine, leucine and isoleucine degradation - Sus scrofa (pig)
Class
Metabolism; Amino acid metabolism
Pathway map
ssc00280  Valine, leucine and isoleucine degradation
ssc00280

Module
ssc_M00036  Leucine degradation, leucine => acetoacetate + acetyl-CoA [PATH:ssc00280]
ssc_M00741  Propanoyl-CoA metabolism, propanoyl-CoA => succinyl-CoA [PATH:ssc00280]
Other DBs
GO: 0006550 0006552 0006574
Organism
Sus scrofa (pig) [GN:ssc]
Gene
100037986  MCEE; methylmalonyl-CoA epimerase, mitochondrial [KO:K05606] [EC:5.1.99.1]
100142666  BCKDHA; 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial [KO:K00166] [EC:1.2.4.4]
100142669  BCKDHB; 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial [KO:K00167] [EC:1.2.4.4]
100152303  ACAT2; acetyl-CoA acetyltransferase, cytosolic [KO:K00626] [EC:2.3.1.9]
100153301  ALDH6A1; methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial isoform X1 [KO:K00140] [EC:1.2.1.18 1.2.1.27]
100153809  ALDH9A1; 4-trimethylaminobutyraldehyde dehydrogenase isoform X1 [KO:K00149] [EC:1.2.1.47 1.2.1.3]
100154810  ACADSB; short/branched chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K09478] [EC:1.3.8.5]
100155020  AUH; methylglutaconyl-CoA hydratase, mitochondrial isoform X1 [KO:K05607] [EC:4.2.1.18]
100156047  IVD; isovaleryl-CoA dehydrogenase, mitochondrial [KO:K00253] [EC:1.3.8.4]
100156278  ALDH1B1; aldehyde dehydrogenase X, mitochondrial [KO:K00128] [EC:1.2.1.3]
100156530  DBT; lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial isoform X2 [KO:K09699] [EC:2.3.1.168]
100156545  AACS; acetoacetyl-CoA synthetase [KO:K01907] [EC:6.2.1.16]
100156927  ECHS1; enoyl-CoA hydratase, mitochondrial [KO:K07511] [EC:4.2.1.17]
100158147  PCCB; propionyl-CoA carboxylase beta chain, mitochondrial precursor [KO:K01966] [EC:6.4.1.3 2.1.3.15]
100312959  ACAA2; 3-ketoacyl-CoA thiolase, mitochondrial [KO:K07508] [EC:2.3.1.16]
100513890  AGXT2; alanine--glyoxylate aminotransferase 2, mitochondrial [KO:K00827] [EC:2.6.1.44 2.6.1.40]
100514687  HIBCH; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial isoform X1 [KO:K05605] [EC:3.1.2.4]
100515577  ACAA1; 3-ketoacyl-CoA thiolase, peroxisomal isoform X1 [KO:K07513] [EC:2.3.1.16]
100516656  HIBADH; 3-hydroxyisobutyrate dehydrogenase, mitochondrial [KO:K00020] [EC:1.1.1.31]
100518224  MCCC2; methylcrotonoyl-CoA carboxylase beta chain, mitochondrial [KO:K01969] [EC:6.4.1.4]
100518784  BCAT1; branched-chain-amino-acid aminotransferase, cytosolic isoform X1 [KO:K00826] [EC:2.6.1.42]
100522257  IL4I1; L-amino-acid oxidase isoform X1 [KO:K03334] [EC:1.4.3.2]
100523701  AOX1; aldehyde oxidase [KO:K00157] [EC:1.2.3.1]
100524103  PCCA; propionyl-CoA carboxylase alpha chain, mitochondrial isoform X1 [KO:K01965] [EC:6.4.1.3]
100524223  HMGCS1; hydroxymethylglutaryl-CoA synthase, cytoplasmic [KO:K01641] [EC:2.3.3.10]
100524293  HSD17B10; 3-hydroxyacyl-CoA dehydrogenase type-2 isoform X2 [KO:K08683] [EC:1.1.1.35 1.1.1.178]
100524382  [KO:K03334] [EC:1.4.3.2]
100525099  [KO:K03334] [EC:1.4.3.2]
100525303  ALDH3A2; fatty aldehyde dehydrogenase isoform X2 [KO:K00128] [EC:1.2.1.3]
100525616  AOX2; aldehyde oxidase 2 [KO:K00157] [EC:1.2.3.1]
100621218  HMGCL; hydroxymethylglutaryl-CoA lyase, mitochondrial isoform X2 [KO:K01640] [EC:4.1.3.4]
100623394  AOX4; aldehyde oxidase 4 [KO:K00157] [EC:1.2.3.1]
100624482  MCCC1; methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial isoform X1 [KO:K01968] [EC:6.4.1.4]
100626793  ACAT1; acetyl-CoA acetyltransferase, mitochondrial isoform X1 [KO:K00626] [EC:2.3.1.9]
100627341  ACAD8; isobutyryl-CoA dehydrogenase, mitochondrial [KO:K11538] [EC:1.3.99.-]
100627473  HMGCLL1; 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic isoform X1 [KO:K01640] [EC:4.1.3.4]
100739500  ACSF3; acyl-CoA synthetase family member 3, mitochondrial isoform X1 [KO:K18660] [EC:6.2.1.76 6.2.1.-]
106504110  ALDH7A1; alpha-aminoadipic semialdehyde dehydrogenase [KO:K14085] [EC:1.2.1.31 1.2.1.8 1.2.1.3]
110260333  [KO:K01641] [EC:2.3.3.10]
396841  BCAT2; branched-chain-amino-acid aminotransferase, mitochondrial isoform X3 [KO:K00826] [EC:2.6.1.42]
396932  ACADS; short-chain specific acyl-CoA dehydrogenase, mitochondrial precursor [KO:K00248] [EC:1.3.8.1]
396978  OXCT1; succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial precursor [KO:K01027] [EC:2.8.3.5]
397012  HADHA; trifunctional enzyme subunit alpha, mitochondrial [KO:K07515] [EC:4.2.1.17 1.1.1.211]
397017  HADHB; trifunctional enzyme subunit beta, mitochondrial [KO:K07509] [EC:2.3.1.16]
397104  ACADM; medium-chain specific acyl-CoA dehydrogenase, mitochondrial precursor [KO:K00249] [EC:1.3.8.7]
397129  DLD; dihydrolipoyl dehydrogenase, mitochondrial precursor [KO:K00382] [EC:1.8.1.4]
397500  ABAT; 4-aminobutyrate aminotransferase, mitochondrial [KO:K13524] [EC:2.6.1.19 2.6.1.22]
397604  HADH; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial precursor [KO:K00022] [EC:1.1.1.35]
397673  HMGCS2; hydroxymethylglutaryl-CoA synthase, mitochondrial precursor [KO:K01641] [EC:2.3.3.10]
399535  MUT; methylmalonyl-CoA mutase, mitochondrial precursor [KO:K01847] [EC:5.4.99.2]
448846  EHHADH; peroxisomal bifunctional enzyme [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
733685  ALDH2; aldehyde dehydrogenase, mitochondrial precursor [KO:K00128] [EC:1.2.1.3]
Compound
C00024  Acetyl-CoA
C00068  Thiamin diphosphate
C00091  Succinyl-CoA
C00100  Propanoyl-CoA
C00123  L-Leucine
C00141  3-Methyl-2-oxobutanoic acid
C00164  Acetoacetate
C00183  L-Valine
C00233  4-Methyl-2-oxopentanoate
C00332  Acetoacetyl-CoA
C00349  2-Methyl-3-oxopropanoate
C00356  (S)-3-Hydroxy-3-methylglutaryl-CoA
C00407  L-Isoleucine
C00630  2-Methylpropanoyl-CoA
C00671  (S)-3-Methyl-2-oxopentanoic acid
C00683  (S)-Methylmalonyl-CoA
C01205  (R)-3-Amino-2-methylpropanoate
C01213  (R)-Methylmalonyl-CoA
C02170  Methylmalonate
C02939  3-Methylbutanoyl-CoA
C03069  3-Methylcrotonyl-CoA
C03231  3-Methylglutaconyl-CoA
C03284  L-3-Aminoisobutanoate
C03344  2-Methylacetoacetyl-CoA
C03345  2-Methylbut-2-enoyl-CoA
C03460  2-Methylprop-2-enoyl-CoA
C04405  (2S,3S)-3-Hydroxy-2-methylbutanoyl-CoA
C05996  Branched chain fatty acid
C05998  3-Hydroxyisovaleryl-CoA
C06000  (S)-3-Hydroxyisobutyryl-CoA
C06001  (S)-3-Hydroxyisobutyrate
C06002  (S)-Methylmalonate semialdehyde
C15972  Enzyme N6-(lipoyl)lysine
C15973  Enzyme N6-(dihydrolipoyl)lysine
C15974  3-Methyl-1-hydroxybutyl-ThPP
C15975  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(3-methylbutanoyl)dihydrolipoyllysine
C15976  2-Methyl-1-hydroxypropyl-ThPP
C15977  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine
C15978  2-Methyl-1-hydroxybutyl-ThPP
C15979  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylbutanoyl)dihydrolipoyllysine
C15980  (S)-2-Methylbutanoyl-CoA
C20827  3-Hydroxyisovalerate
Related
pathway
ssc00020  Citrate cycle (TCA cycle)
ssc00240  Pyrimidine metabolism
ssc00290  Valine, leucine and isoleucine biosynthesis
ssc00640  Propanoate metabolism
ssc00900  Terpenoid backbone biosynthesis
KO pathway
ko00280   

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