KEGG   PATHWAY: one00280
Entry
one00280                    Pathway                                
Name
Valine, leucine and isoleucine degradation - Oncorhynchus nerka (sockeye salmon)
Class
Metabolism; Amino acid metabolism
Pathway map
one00280  Valine, leucine and isoleucine degradation
one00280

Other DBs
GO: 0006550 0006552 0006574
Organism
Oncorhynchus nerka (sockeye salmon) [GN:one]
Gene
115102563  [KO:K00128] [EC:1.2.1.3]
115102664  [KO:K00128] [EC:1.2.1.3]
115106020  agxt2; alanine--glyoxylate aminotransferase 2, mitochondrial [KO:K00827] [EC:2.6.1.44 2.6.1.40]
115106398  [KO:K00167] [EC:1.2.4.4]
115106814  [KO:K00128] [EC:1.2.1.3]
115106986  bcat1; branched-chain-amino-acid aminotransferase, cytosolic [KO:K00826] [EC:2.6.1.42]
115107953  hibch; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial isoform X1 [KO:K05605] [EC:3.1.2.4]
115107986  [KO:K00140] [EC:1.2.1.18 1.2.1.27]
115108009  mmut; LOW QUALITY PROTEIN: methylmalonyl-CoA mutase, mitochondrial [KO:K01847] [EC:5.4.99.2]
115108145  [KO:K09699] [EC:2.3.1.168]
115108416  [KO:K01969] [EC:6.4.1.4]
115108456  [KO:K01968] [EC:6.4.1.4]
115108629  aldh9a1; 4-trimethylaminobutyraldehyde dehydrogenase isoform X1 [KO:K00149] [EC:1.2.1.47 1.2.1.3]
115109103  [KO:K09699] [EC:2.3.1.168]
115110049  aldh16a1; aldehyde dehydrogenase family 16 member A1 [KO:K00128] [EC:1.2.1.3]
115111247  aacs; acetoacetyl-CoA synthetase [KO:K01907] [EC:6.2.1.16]
115111718  [KO:K07508] [EC:2.3.1.16]
115111874  oxct1; succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial isoform X1 [KO:K01027] [EC:2.8.3.5]
115112171  [KO:K05606] [EC:5.1.99.1]
115113044  [KO:K01640] [EC:4.1.3.4]
115113588  acsf3; acyl-CoA synthetase family member 3, mitochondrial isoform X1 [KO:K18660] [EC:6.2.1.76 6.2.1.-]
115113594  [KO:K05606] [EC:5.1.99.1]
115114631  [KO:K00149] [EC:1.2.1.47 1.2.1.3]
115117879  auh; methylglutaconyl-CoA hydratase, mitochondrial isoform X1 [KO:K05607] [EC:4.2.1.18]
115118093  [KO:K01641] [EC:2.3.3.10]
115118459  aldh7a1; alpha-aminoadipic semialdehyde dehydrogenase [KO:K14085] [EC:1.2.1.31 1.2.1.8 1.2.1.3]
115120885  acads; short-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00248] [EC:1.3.8.1]
115121047  acaa1; 3-ketoacyl-CoA thiolase, peroxisomal isoform X1 [KO:K07513] [EC:2.3.1.16]
115121058  [KO:K00826] [EC:2.6.1.42]
115121664  [KO:K00826] [EC:2.6.1.42]
115121742  ehhadh; peroxisomal bifunctional enzyme [KO:K07514] [EC:4.2.1.17 1.1.1.35 5.3.3.8]
115122832  hadhb; trifunctional enzyme subunit beta, mitochondrial [KO:K07509] [EC:2.3.1.16]
115123733  acadm; medium-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00249] [EC:1.3.8.7]
115124881  [KO:K00128] [EC:1.2.1.3]
115125326  [KO:K00128] [EC:1.2.1.3]
115125423  [KO:K01966] [EC:6.4.1.3 2.1.3.15]
115125505  [KO:K01966] [EC:6.4.1.3 2.1.3.15]
115126100  [KO:K08683] [EC:1.1.1.35 1.1.1.178]
115126486  hadh; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial [KO:K00022] [EC:1.1.1.35]
115129275  [KO:K00128] [EC:1.2.1.3]
115129646  [KO:K00157] [EC:1.2.3.1]
115129647  [KO:K00157] [EC:1.2.3.1]
115131279  [KO:K00020] [EC:1.1.1.31]
115134466  [KO:K00382] [EC:1.8.1.4]
115134799  [KO:K03334] [EC:1.4.3.2]
115135357  echs1; enoyl-CoA hydratase, mitochondrial [KO:K07511] [EC:4.2.1.17]
115135873  acat1; acetyl-CoA acetyltransferase, mitochondrial [KO:K00626] [EC:2.3.1.9]
115136711  acad8; isobutyryl-CoA dehydrogenase, mitochondrial isoform X1 [KO:K11538] [EC:1.3.99.-]
115138409  [KO:K01640] [EC:4.1.3.4]
115138738  [KO:K07515] [EC:4.2.1.17 1.1.1.211]
115139206  [KO:K00140] [EC:1.2.1.18 1.2.1.27]
115139309  acat2; acetyl-CoA acetyltransferase, cytosolic [KO:K00626] [EC:2.3.1.9]
115140188  [KO:K07508] [EC:2.3.1.16]
115140704  [KO:K01027] [EC:2.8.3.5]
115141388  [KO:K00167] [EC:1.2.4.4]
115141709  [KO:K03334] [EC:1.4.3.2]
115144398  [KO:K01640] [EC:4.1.3.4]
115144793  [KO:K00382] [EC:1.8.1.4]
115145044  [KO:K01968] [EC:6.4.1.4]
115145942  [KO:K07515] [EC:4.2.1.17 1.1.1.211]
115146212  aldh6a1; methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial isoform X1 [KO:K00140] [EC:1.2.1.18 1.2.1.27]
115146315  [KO:K01640] [EC:4.1.3.4]
115146468  ivd; isovaleryl-CoA dehydrogenase, mitochondrial [KO:K00253] [EC:1.3.8.4]
115147012  [KO:K01027] [EC:2.8.3.5]
Compound
C00024  Acetyl-CoA
C00068  Thiamin diphosphate
C00091  Succinyl-CoA
C00100  Propanoyl-CoA
C00123  L-Leucine
C00141  3-Methyl-2-oxobutanoic acid
C00164  Acetoacetate
C00183  L-Valine
C00233  4-Methyl-2-oxopentanoate
C00332  Acetoacetyl-CoA
C00349  2-Methyl-3-oxopropanoate
C00356  (S)-3-Hydroxy-3-methylglutaryl-CoA
C00407  L-Isoleucine
C00630  2-Methylpropanoyl-CoA
C00671  (S)-3-Methyl-2-oxopentanoic acid
C00683  (S)-Methylmalonyl-CoA
C01205  (R)-3-Amino-2-methylpropanoate
C01213  (R)-Methylmalonyl-CoA
C02170  Methylmalonate
C02939  3-Methylbutanoyl-CoA
C03069  3-Methylcrotonyl-CoA
C03231  3-Methylglutaconyl-CoA
C03284  L-3-Aminoisobutanoate
C03344  2-Methylacetoacetyl-CoA
C03345  2-Methylbut-2-enoyl-CoA
C03460  2-Methylprop-2-enoyl-CoA
C04405  (2S,3S)-3-Hydroxy-2-methylbutanoyl-CoA
C05996  Branched chain fatty acid
C05998  3-Hydroxyisovaleryl-CoA
C06000  (S)-3-Hydroxyisobutyryl-CoA
C06001  (S)-3-Hydroxyisobutyrate
C06002  (S)-Methylmalonate semialdehyde
C15972  Enzyme N6-(lipoyl)lysine
C15973  Enzyme N6-(dihydrolipoyl)lysine
C15974  3-Methyl-1-hydroxybutyl-ThPP
C15975  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(3-methylbutanoyl)dihydrolipoyllysine
C15976  2-Methyl-1-hydroxypropyl-ThPP
C15977  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine
C15978  2-Methyl-1-hydroxybutyl-ThPP
C15979  [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylbutanoyl)dihydrolipoyllysine
C15980  (S)-2-Methylbutanoyl-CoA
C20827  3-Hydroxyisovalerate
Related
pathway
one00020  Citrate cycle (TCA cycle)
one00240  Pyrimidine metabolism
one00290  Valine, leucine and isoleucine biosynthesis
one00640  Propanoate metabolism
one00900  Terpenoid backbone biosynthesis
KO pathway
ko00280   

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