| | PATHWAY: ptr00280 | |
Entry |
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Name |
Valine, leucine and isoleucine degradation - Pan troglodytes (chimpanzee) |
Class |
Metabolism; Amino acid metabolism
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Pathway map |
ptr00280 | Valine, leucine and isoleucine degradation |
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Module |
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Other DBs |
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Organism |
Pan troglodytes (chimpanzee) [GN: ptr]
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Gene |
465345 | BCAT1; branched-chain-amino-acid aminotransferase, cytosolic isoform X1 [KO:K00826] [EC:2.6.1.42] |
456189 | BCAT2; branched-chain-amino-acid aminotransferase, mitochondrial isoform X5 [KO:K00826] [EC:2.6.1.42] |
468889 | BCKDHA; 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial precursor [KO:K00166] [EC:1.2.4.4] |
462845 | BCKDHB; 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial isoform X1 [KO:K00167] [EC:1.2.4.4] |
457056 | DBT; lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial [KO:K09699] [EC:2.3.1.168] |
742921 | ACADS; short-chain specific acyl-CoA dehydrogenase, mitochondrial [KO:K00248] [EC:1.3.8.1] |
469356 | ACADM; medium-chain specific acyl-CoA dehydrogenase, mitochondrial precursor [KO:K00249] [EC:1.3.8.7] |
745464 | ACADSB; short/branched chain specific acyl-CoA dehydrogenase, mitochondrial isoform X2 [KO:K09478] [EC:1.3.8.5] |
451683 | ACAD8; isobutyryl-CoA dehydrogenase, mitochondrial isoform X3 [KO:K11538] [EC:1.3.99.-] |
461424 | HADH; hydroxyacyl-coenzyme A dehydrogenase, mitochondrial isoform X1 [KO:K00022] [EC:1.1.1.35] |
738775 | PCCA; propionyl-CoA carboxylase alpha chain, mitochondrial isoform X1 [KO:K01965] [EC:6.4.1.3] |
459828 | HIBCH; 3-hydroxyisobutyryl-CoA hydrolase, mitochondrial isoform X5 [KO:K05605] [EC:3.1.2.4] |
463313 | HIBADH; 3-hydroxyisobutyrate dehydrogenase, mitochondrial isoform X2 [KO:K00020] [EC:1.1.1.31] |
467506 | ALDH6A1; methylmalonate-semialdehyde/malonate-semialdehyde dehydrogenase [acylating], mitochondrial [KO:K00140] [EC:1.2.1.18 1.2.1.27] |
454311 | ACSF3; malonate--CoA ligase ACSF3, mitochondrial isoform X7 [KO:K18660] [EC:6.2.1.76 6.2.1.-] |
460872 | MCCC1; methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial isoform X2 [KO:K01968] [EC:6.4.1.4] |
461823 | MCCC2; methylcrotonoyl-CoA carboxylase beta chain, mitochondrial isoform X3 [KO:K01969] [EC:6.4.1.4] |
456624 | HMGCL; hydroxymethylglutaryl-CoA lyase, mitochondrial isoform X1 [KO:K01640] [EC:4.1.3.4] |
742364 | HMGCLL1; 3-hydroxymethyl-3-methylglutaryl-CoA lyase, cytoplasmic isoform X1 [KO:K01640] [EC:4.1.3.4] |
737468 | OXCT1; succinyl-CoA:3-ketoacid coenzyme A transferase 1, mitochondrial [KO:K01027] [EC:2.8.3.5] |
456780 | OXCT2; succinyl-CoA:3-ketoacid coenzyme A transferase 2, mitochondrial [KO:K01027] [EC:2.8.3.5] |
112209812 | LOW QUALITY PROTEIN: succinyl-CoA:3-ketoacid coenzyme A transferase 2, mitochondrial-like [KO:K01027] [EC:2.8.3.5] |
|
Compound |
C00141 | 3-Methyl-2-oxobutanoic acid |
C00233 | 4-Methyl-2-oxopentanoate |
C00349 | 2-Methyl-3-oxopropanoate |
C00356 | (S)-3-Hydroxy-3-methylglutaryl-CoA |
C00671 | (S)-3-Methyl-2-oxopentanoic acid |
C01205 | (R)-3-Amino-2-methylpropanoate |
C03344 | 2-Methylacetoacetyl-CoA |
C03345 | 2-Methylbut-2-enoyl-CoA |
C03460 | 2-Methylprop-2-enoyl-CoA |
C04405 | (2S,3S)-3-Hydroxy-2-methylbutanoyl-CoA |
C05996 | Branched chain fatty acid |
C05998 | 3-Hydroxyisovaleryl-CoA |
C06000 | (S)-3-Hydroxyisobutyryl-CoA |
C06001 | (S)-3-Hydroxyisobutyrate |
C06002 | (S)-Methylmalonate semialdehyde |
C15972 | Enzyme N6-(lipoyl)lysine |
C15973 | Enzyme N6-(dihydrolipoyl)lysine |
C15974 | 3-Methyl-1-hydroxybutyl-ThPP |
C15975 | [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(3-methylbutanoyl)dihydrolipoyllysine |
C15976 | 2-Methyl-1-hydroxypropyl-ThPP |
C15977 | [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylpropanoyl)dihydrolipoyllysine |
C15978 | 2-Methyl-1-hydroxybutyl-ThPP |
C15979 | [Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase] S-(2-methylbutanoyl)dihydrolipoyllysine |
C15980 | (S)-2-Methylbutanoyl-CoA |
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Related pathway |
ptr00290 | Valine, leucine and isoleucine biosynthesis |
ptr00900 | Terpenoid backbone biosynthesis |
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KO pathway |
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LinkDB |
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