Entry |
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Symbol |
SCN1A, DEE6, DEE6A, DEE6B, DRVT, EIEE6, FEB3, FEB3A, FHM3, GEFSP2, HBSCI, NAC1, Nav1.1, SCN1, SMEI
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Name |
(RefSeq) sodium voltage-gated channel alpha subunit 1
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KO |
K04833 | voltage-gated sodium channel type I alpha |
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Organism |
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Pathway |
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Disease |
H00606 | Early infantile epileptic encephalopathy |
H01815 | Malignant migrating partial seizures in infancy |
H02564 | Generalized epilepsy with febrile seizures plus |
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Drug target |
Ethyl piperidinoacetylaminobenzoate: | D01519 |
Indecainide hydrochloride: | D04521 |
Levosemotiadil fumarate: | D09833 |
p-Butylaminobenzoyldiethylaminoethyl hydrochloride: | D01967 |
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Brite |
KEGG Orthology (KO) [BR:hsa00001]
09150 Organismal Systems
09156 Nervous system
04728 Dopaminergic synapse
6323 (SCN1A)
09180 Brite Hierarchies
09183 Protein families: signaling and cellular processes
04040 Ion channels [BR:hsa04040]
6323 (SCN1A)
Ion channels [BR:hsa04040]
Voltage-gated cation channels
Sodium channel, voltage-gated (Nav)
6323 (SCN1A)
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SSDB |
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Motif |
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Other DBs |
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Structure |
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LinkDB |
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Position |
2:complement(165984641..166149161)
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AA seq |
2009 aa
MEQTVLVPPGPDSFNFFTRESLAAIERRIAEEKAKNPKPDKKDDDENGPKPNSDLEAGKN
LPFIYGDIPPEMVSEPLEDLDPYYINKKTFIVLNKGKAIFRFSATSALYILTPFNPLRKI
AIKILVHSLFSMLIMCTILTNCVFMTMSNPPDWTKNVEYTFTGIYTFESLIKIIARGFCL
EDFTFLRDPWNWLDFTVITFAYVTEFVDLGNVSALRTFRVLRALKTISVIPGLKTIVGAL
IQSVKKLSDVMILTVFCLSVFALIGLQLFMGNLRNKCIQWPPTNASLEEHSIEKNITVNY
NGTLINETVFEFDWKSYIQDSRYHYFLEGFLDALLCGNSSDAGQCPEGYMCVKAGRNPNY
GYTSFDTFSWAFLSLFRLMTQDFWENLYQLTLRAAGKTYMIFFVLVIFLGSFYLINLILA
VVAMAYEEQNQATLEEAEQKEAEFQQMIEQLKKQQEAAQQAATATASEHSREPSAAGRLS
DSSSEASKLSSKSAKERRNRRKKRKQKEQSGGEEKDEDEFQKSESEDSIRRKGFRFSIEG
NRLTYEKRYSSPHQSLLSIRGSLFSPRRNSRTSLFSFRGRAKDVGSENDFADDEHSTFED
NESRRDSLFVPRRHGERRNSNLSQTSRSSRMLAVFPANGKMHSTVDCNGVVSLVGGPSVP
TSPVGQLLPEVIIDKPATDDNGTTTETEMRKRRSSSFHVSMDFLEDPSQRQRAMSIASIL
TNTVEELEESRQKCPPCWYKFSNIFLIWDCSPYWLKVKHVVNLVVMDPFVDLAITICIVL
NTLFMAMEHYPMTDHFNNVLTVGNLVFTGIFTAEMFLKIIAMDPYYYFQEGWNIFDGFIV
TLSLVELGLANVEGLSVLRSFRLLRVFKLAKSWPTLNMLIKIIGNSVGALGNLTLVLAII
VFIFAVVGMQLFGKSYKDCVCKIASDCQLPRWHMNDFFHSFLIVFRVLCGEWIETMWDCM
EVAGQAMCLTVFMMVMVIGNLVVLNLFLALLLSSFSADNLAATDDDNEMNNLQIAVDRMH
KGVAYVKRKIYEFIQQSFIRKQKILDEIKPLDDLNNKKDSCMSNHTAEIGKDLDYLKDVN
GTTSGIGTGSSVEKYIIDESDYMSFINNPSLTVTVPIAVGESDFENLNTEDFSSESDLEE
SKEKLNESSSSSEGSTVDIGAPVEEQPVVEPEETLEPEACFTEGCVQRFKCCQINVEEGR
GKQWWNLRRTCFRIVEHNWFETFIVFMILLSSGALAFEDIYIDQRKTIKTMLEYADKVFT
YIFILEMLLKWVAYGYQTYFTNAWCWLDFLIVDVSLVSLTANALGYSELGAIKSLRTLRA
LRPLRALSRFEGMRVVVNALLGAIPSIMNVLLVCLIFWLIFSIMGVNLFAGKFYHCINTT
TGDRFDIEDVNNHTDCLKLIERNETARWKNVKVNFDNVGFGYLSLLQVATFKGWMDIMYA
AVDSRNVELQPKYEESLYMYLYFVIFIIFGSFFTLNLFIGVIIDNFNQQKKKFGGQDIFM
TEEQKKYYNAMKKLGSKKPQKPIPRPGNKFQGMVFDFVTRQVFDISIMILICLNMVTMMV
ETDDQSEYVTTILSRINLVFIVLFTGECVLKLISLRHYYFTIGWNIFDFVVVILSIVGMF
LAELIEKYFVSPTLFRVIRLARIGRILRLIKGAKGIRTLLFALMMSLPALFNIGLLLFLV
MFIYAIFGMSNFAYVKREVGIDDMFNFETFGNSMICLFQITTSAGWDGLLAPILNSKPPD
CDPNKVNPGSSVKGDCGNPSVGIFFFVSYIIISFLVVVNMYIAVILENFSVATEESAEPL
SEDDFEMFYEVWEKFDPDATQFMEFEKLSQFAAALEPPLNLPQPNKLQLIAMDLPMVSGD
RIHCLDILFAFTKRVLGESGEMDALRIQMEERFMASNPSKVSYQPITTTLKRKQEEVSAV
IIQRAYRRHLLKRTVKQASFTYNKNKIKGGANLLIKEDMIIDRINENSITEKTDLTMSTA
ACPPSYDRVTKPIVEKHEQEGKDEKAKGK |
NT seq |
6030 nt +upstreamnt +downstreamnt
atggagcaaacagtgcttgtaccaccaggacctgacagcttcaacttcttcaccagagaa
tctcttgcggctattgaaagacgcattgcagaagaaaaggcaaagaatcccaaaccagac
aaaaaagatgacgacgaaaatggcccaaagccaaatagtgacttggaagctggaaagaac
cttccatttatttatggagacattcctccagagatggtgtcagagcccctggaggacctg
gacccctactatatcaataagaaaacttttatagtattgaataaagggaaggccatcttc
cggttcagtgccacctctgccctgtacattttaactcccttcaatcctcttaggaaaata
gctattaagattttggtacattcattattcagcatgctaattatgtgcactattttgaca
aactgtgtgtttatgacaatgagtaaccctcctgattggacaaagaatgtagaatacacc
ttcacaggaatatatacttttgaatcacttataaaaattattgcaaggggattctgttta
gaagattttactttccttcgggatccatggaactggctcgatttcactgtcattacattt
gcgtacgtcacagagtttgtggacctgggcaatgtctcggcattgagaacattcagagtt
ctccgagcattgaagacgatttcagtcattccaggcctgaaaaccattgtgggagccctg
atccagtctgtgaagaagctctcagatgtaatgatcctgactgtgttctgtctgagcgta
tttgctctaattgggctgcagctgttcatgggcaacctgaggaataaatgtatacaatgg
cctcccaccaatgcttccttggaggaacatagtatagaaaagaatataactgtgaattat
aatggtacacttataaatgaaactgtctttgagtttgactggaagtcatatattcaagat
tcaagatatcattatttcctggagggttttttagatgcactactatgtggaaatagctct
gatgcaggccaatgtccagagggatatatgtgtgtgaaagctggtagaaatcccaattat
ggctacacaagctttgataccttcagttgggcttttttgtccttgtttcgactaatgact
caggacttctgggaaaatctttatcaactgacattacgtgctgctgggaaaacgtacatg
atattttttgtattggtcattttcttgggctcattctacctaataaatttgatcctggct
gtggtggccatggcctacgaggaacagaatcaggccaccttggaagaagcagaacagaaa
gaggccgaatttcagcagatgattgaacagcttaaaaagcaacaggaggcagctcagcag
gcagcaacggcaactgcctcagaacattccagagagcccagtgcagcaggcaggctctca
gacagctcatctgaagcctctaagttgagttccaagagtgctaaggaaagaagaaatcgg
aggaagaaaagaaaacagaaagagcagtctggtggggaagagaaagatgaggatgaattc
caaaaatctgaatctgaggacagcatcaggaggaaaggttttcgcttctccattgaaggg
aaccgattgacatatgaaaagaggtactcctccccacaccagtctttgttgagcatccgt
ggctccctattttcaccaaggcgaaatagcagaacaagccttttcagctttagagggcga
gcaaaggatgtgggatctgagaacgacttcgcagatgatgagcacagcacctttgaggat
aacgagagccgtagagattccttgtttgtgccccgacgacacggagagagacgcaacagc
aacctgagtcagaccagtaggtcatcccggatgctggcagtgtttccagcgaatgggaag
atgcacagcactgtggattgcaatggtgtggtttccttggttggtggaccttcagttcct
acatcgcctgttggacagcttctgccagaggtgataatagataagccagctactgatgac
aatggaacaaccactgaaactgaaatgagaaagagaaggtcaagttctttccacgtttcc
atggactttctagaagatccttcccaaaggcaacgagcaatgagtatagccagcattcta
acaaatacagtagaagaacttgaagaatccaggcagaaatgcccaccctgttggtataaa
ttttccaacatattcttaatctgggactgttctccatattggttaaaagtgaaacatgtt
gtcaacctggttgtgatggacccatttgttgacctggccatcaccatctgtattgtctta
aatactcttttcatggccatggagcactatccaatgacggaccatttcaataatgtgctt
acagtaggaaacttggttttcactgggatctttacagcagaaatgtttctgaaaattatt
gccatggatccttactattatttccaagaaggctggaatatctttgacggttttattgtg
acgcttagcctggtagaacttggactcgccaatgtggaaggattatctgttctccgttca
tttcgattgctgcgagttttcaagttggcaaaatcttggccaacgttaaatatgctaata
aagatcatcggcaattccgtgggggctctgggaaatttaaccctcgtcttggccatcatc
gtcttcatttttgccgtggtcggcatgcagctctttggtaaaagctacaaagattgtgtc
tgcaagatcgccagtgattgtcaactcccacgctggcacatgaatgacttcttccactcc
ttcctgattgtgttccgcgtgctgtgtggggagtggatagagaccatgtgggactgtatg
gaggttgctggtcaagccatgtgccttactgtcttcatgatggtcatggtgattggaaac
ctagtggtcctgaatctctttctggccttgcttctgagctcatttagtgcagacaacctt
gcagccactgatgatgataatgaaatgaataatctccaaattgctgtggataggatgcac
aaaggagtagcttatgtgaaaagaaaaatatatgaatttattcaacagtccttcattagg
aaacaaaagattttagatgaaattaaaccacttgatgatctaaacaacaagaaagacagt
tgtatgtccaatcatacagcagaaattgggaaagatcttgactatcttaaagatgtaaat
ggaactacaagtggtataggaactggcagcagtgttgaaaaatacattattgatgaaagt
gattacatgtcattcataaacaaccccagtcttactgtgactgtaccaattgctgtagga
gaatctgactttgaaaatttaaacacggaagactttagtagtgaatcggatctggaagaa
agcaaagagaaactgaatgaaagcagtagctcatcagaaggtagcactgtggacatcggc
gcacctgtagaagaacagcccgtagtggaacctgaagaaactcttgaaccagaagcttgt
ttcactgaaggctgtgtacaaagattcaagtgttgtcaaatcaatgtggaagaaggcaga
ggaaaacaatggtggaacctgagaaggacgtgtttccgaatagttgaacataactggttt
gagaccttcattgttttcatgattctccttagtagtggtgctctggcatttgaagatata
tatattgatcagcgaaagacgattaagacgatgttggaatatgctgacaaggttttcact
tacattttcattctggaaatgcttctaaaatgggtggcatatggctatcaaacatatttc
accaatgcctggtgttggctggacttcttaattgttgatgtttcattggtcagtttaaca
gcaaatgccttgggttactcagaacttggagccatcaaatctctcaggacactaagagct
ctgagacctctaagagccttatctcgatttgaagggatgagggtggttgtgaatgccctt
ttaggagcaattccatccatcatgaatgtgcttctggtttgtcttatattctggctaatt
ttcagcatcatgggcgtaaatttgtttgctggcaaattctaccactgtattaacaccaca
actggtgacaggtttgacatcgaagacgtgaataatcatactgattgcctaaaactaata
gaaagaaatgagactgctcgatggaaaaatgtgaaagtaaactttgataatgtaggattt
gggtatctctctttgcttcaagttgccacattcaaaggatggatggatataatgtatgca
gcagttgattccagaaatgtggaactccagcctaagtatgaagaaagtctgtacatgtat
ctttactttgttattttcatcatctttgggtccttcttcaccttgaacctgtttattggt
gtcatcatagataatttcaaccagcagaaaaagaagtttggaggtcaagacatctttatg
acagaagaacagaagaaatactataatgcaatgaaaaaattaggatcgaaaaaaccgcaa
aagcctatacctcgaccaggaaacaaatttcaaggaatggtctttgacttcgtaaccaga
caagtttttgacataagcatcatgattctcatctgtcttaacatggtcacaatgatggtg
gaaacagatgaccagagtgaatatgtgactaccattttgtcacgcatcaatctggtgttc
attgtgctatttactggagagtgtgtactgaaactcatctctctacgccattattatttt
accattggatggaatatttttgattttgtggttgtcattctctccattgtaggtatgttt
cttgccgagctgatagaaaagtatttcgtgtcccctaccctgttccgagtgatccgtctt
gctaggattggccgaatcctacgtctgatcaaaggagcaaaggggatccgcacgctgctc
tttgctttgatgatgtcccttcctgcgttgtttaacatcggcctcctactcttcctagtc
atgttcatctacgccatctttgggatgtccaactttgcctatgttaagagggaagttggg
atcgatgacatgttcaactttgagacctttggcaacagcatgatctgcctattccaaatt
acaacctctgctggctgggatggattgctagcacccattctcaacagtaagccacccgac
tgtgaccctaataaagttaaccctggaagctcagttaagggagactgtgggaacccatct
gttggaattttcttttttgtcagttacatcatcatatccttcctggttgtggtgaacatg
tacatcgcggtcatcctggagaacttcagtgttgctactgaagaaagtgcagagcctctg
agtgaggatgactttgagatgttctatgaggtttgggagaagtttgatcccgatgcaact
cagttcatggaatttgaaaaattatctcagtttgcagctgcgcttgaaccgcctctcaat
ctgccacaaccaaacaaactccagctcattgccatggatttgcccatggtgagtggtgac
cggatccactgtcttgatatcttatttgcttttacaaagcgggttctaggagagagtgga
gagatggatgctctacgaatacagatggaagagcgattcatggcttccaatccttccaag
gtctcctatcagccaatcactactactttaaaacgaaaacaagaggaagtatctgctgtc
attattcagcgtgcttacagacgccaccttttaaagcgaactgtaaaacaagcttccttt
acgtacaataaaaacaaaatcaaaggtggggctaatcttcttataaaagaagacatgata
attgacagaataaatgaaaactctattacagaaaaaactgatctgaccatgtccactgca
gcttgtccaccttcctatgaccgggtgacaaagccaattgtggaaaaacatgagcaagaa
ggcaaagatgaaaaagccaaagggaaataa |